Fabry disease previously diagnosed as Henoch-Schonlein purpura

Henoch-Schonlein purpura (HSP) is a generalized vasculitis characterized by manifestations of the skin, joints, gastrointestinal tract, and renal involvement. Although HSP can occur at any age and is usually a self-limited disease in children, it is less common and has a poor prognosis in adults. Renal involvement affects approximately one-third of HSP patients, and varies from intermittent hematuria and proteinuria, to severe nephrotic-nephritic syndrome with kidney histology being identical to that of immunoglobin A (IgA) nephropathy. KCI Citation Count: 2