Two Cases of Herlyn-Werner-Wunderlich Syndrome in Neonates and Adolescents with Hydrocolpos and Hematocolpometra

The Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital anomaly that is characterized by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It is often diagnosed in patient with pelvic or abdominal pain during puberty. Treatment is basically resection of obstructed vaginal septum by surgical approach. We describe two case of HWW syndrome, one is a neonate who was diagnosed as hydronephrosis and pelvic mass in postnatal ultrasonography, and the other is a 13-year-old girl with abdominal pain.