베체트병 환자에서 발생한 Lenticulostriate 동맥류 파열 1예

베체트병의 환자에서 뇌동맥류는 흔치 않은 중추신경계침범 임상상이며, 특히 lenticulostriate 동맥류가 발생하는 경우는 매우 드물다. 저자들은 활동성 베체트병에의한 lenticulostriate 동맥류 파열로 발생한 급성 좌측 편마비환자에서 고용량 글루코코르티코이드제제 투여로 호전된 국내첫 번째 증례를 경험하였기에 문헌고찰과 함께 보고한다. Behcet`s disease (BD) is characterized by recurrent oro-genital ulcers, skin lesions, and intraocular inflammation, but can also affect various internal organs. Vascular BD usually presents with luminal stenosis, thrombosis, or aneurysm formation in aorta and peripheral arteries. However, intracranial artery involvement has been uncommonly reported in patients with BD and BD cases with lenticulostriate artery aneurysm have been rarely described in the English-language literature. We hereby reported the first case of a Korean BD patient presenting with a ruptured lenticulostriate artery aneurysm, who received medical treatment, and reviewed the literature on reported cases of BD with intracranial aneurysms. (J Rheum Dis 2015;22:317-321)