URGICAL REPAIR WITHOUT VENTRICLOTOMY FOR DOUBLE-CHAMBERED RIGHT VENTRICLE WITH VENTRICULAR SEPTAL DEFECT：A CASE REPORT

Abstract：A 3-year-old boy with double-chambered right ventricle (DCRV), ventricular septal defect (VSD) and pulmonary stenosis underwent successfully surgical correction without a right ventriculotomy. This surgical approach consisted of a combined right atriotomy and pulmonary arteriotomy. A perimenbronous VSD was closed through the tricuspid valve, and the anomalous muscle bands of right ventricular outflow obstruction were resected through both the tricuspid valve and pulmonary valve. The pressure gradient between the right ventricle and pulmonary artery decreased from 70mmHg to 20mmHg. No major complications occurred after the repair. The transatrial approach with pulmonary arteriotomy is an appropriate and effective method to correct a DCRV. 「INTRODUCTION」Double-chambered right ventricle (DCRV) is an uncommon congenital heart disease consisting of one or more anomalous muscle bundles, dividing the right ventricle into a proximal high pressure and a distal low pressure chamber. The first successful surgical repair of this condition was carried out in 1962, by Lucas et al.1), who performed it through a right ventriculotomy. Subsequently Walsh et al.2) and Penkoske et al.3) reported a right transatrial approach in order to avoid a postoperative depression of myocardial performance due to ventriculotomy. We report herein a case of DCRV that was repaired using a combined approach of a right atriotomy and a transverse pulmonary arteriotomy.