급성 구인두 연하곤란으로 발현된 피부근염

저자들은 급성으로 발병한 연하곤란을 주된 증상으로 내원하여 사지의 근육병증이 병발한 피부근염을 경험하였다. 구인두 연하곤란의 적절한 평가에 있어서 고해상도 식도 내압검사를 기존의 검사와 더불어 유용한 검사로 이용할 수 있다고 판단하여 문헌 고찰과 함께 보고한다. Dermatomyositis is a rare autoimmune disorder afflicting an estimated 6-10 million people worldwide that has a distinct clinical entity identified by a characteristic skin rash and inflammatory myopathy. It can be combined with other connective tissue diseases such as systemic sclerosis or systemic lupus erythematosus. In addition to primary disturbances of limb muscle and skin, extramuscular manifestations include dysphagia, cardiac conduction abnormalities, interstitial lung disease or subcutaneous calcifications. Dysphagia occurs in 12%-54% of those with dermatomyositis, manifests gradually over weeks to months rather than in acutely, and is diagnosed with high-resolution esophageal manometry and video-fluoroscopic monitoring during swallowing. We report a case of dermatomyositis presenting initially with acute oropharyngeal dysphagia and review the available swallowing studies and related literature. (Kor J Neurogastroenterol Motil 2009;15:65-69)