소아에 (小兒) 있어서 간담도계의 (肝膽道系) 원발성 (原發性) 악성종양의 (惡性腫瘍) 임상적 (臨床的) 관찰

The clinical data on the patients with primary malignant tumors of the hepatobiliary system from Aug 1968 to Sep 1983 have been reviewed. Eleven patients were hepatoblastoma, 4 patients were hepatocellular carcinoma and 1 patient was embryonal rhabdomyosarcoma occurred in common bile duct. Age incidence of the hepatoblastoma was younger than hepatocellular carcinoma. All 11 patients with hepatoblastoma were less than 3 years old, and 3 of the 4 patients with hepatocellular carcinoma were more than 3 years old. The prognosis of hepatocellular carcinoma occuring in children has been reported as poor, but several long-term survival cases have been reported after surgical resection in the hepatoblastoma. In 8 of the 16 cases, surgical resection was possible. Of the four long-term survivors of the hepatoblastoma, 2 patients has been alive for 10 months and 15 months since diagnosis till now.