AESTHETIC SURGICAL APPROACH FOR STURGE-WEBER SYNDROME AND FACIAL ARTERIOVENOUS TUMORS/ABORDAGEM CIRURGICA ESTETICA DA SINDROME DE STURGE-WEBER E TUMORES ARTERIOVENOSOS FACIAIS/ENFOQUE QUIRURGICO ESTETICO PARA EL SINDROME DE STURGE-WEBER Y TUMORES ARTERIOVENOSOS FACIALES

Introduction: Sturge-Weber Syndrome (SWS) is a rare, congenital neurovascular condition associated with facial cutaneous capillary or venous malformations. The manifestations are intrinsically related to vascular malformations, resulting in neurological symptoms, soft tissue abnormalities, and restricted bone growth. Methodology: This is a case report of a single patient diagnosed with SWS, following the guidelines established by Resolution 466/12 of the National Health Council of Brazil (CNS). Results and Discussion: A Vascular Surgery approach with embolization was performed prior to the Plastic Surgery intervention. It is important to note that this particular patient did not present the common neurological manifestations. Additionally, port-wine stains manifested as giant hemangiomas on the face. Conclusion: A multidisciplinary team is essential for patients with this condition, as it can facilitate surgical resection when vascular studies are performed prior to surgery. Moreover, a multidisciplinary approach is crucial due to the varied clinical presentation and chronic conditions that require treatment. Keywords: Plastic surgery; Sturge-Weber syndrome; hemangioma; vascular surgical procedures. Introducao: A sindrome de Sturge Weber (SSW) e uma condicao neurovascular rara, congenita, associada a malformacoes capilares ou venosas cutaneas faciais, as manifestacoes sao intrinsecamente relacionadas as malformacoes vasculares, que resultam em sintomas neurologicos, anormalidades em partes moles e restricao de crescimento osseo. Metodologia: Trata-se de um relato de caso de um unico paciente com diagnostico da SSW, seguindo as normas estabelecidas pela resolucao 466/12 do Conselho Nacional de Saude. Resultados e Discussao: Realizada abordagem da Cirurgia Vascular com embolizacao previamente a abordagem da Cirurgia Plastica. E importante ressaltar que esse paciente em particular nao tinha as manifestacoes neurologicas comuns. Acresce-se a manchas vinho-porto manifestando-se como hemangiomas gigantes em face. Conclusao: E fundamental a equipe multidisciplinar nos pacientes com essa afeccao, pois podem facilitar a resseccao cirurgica, quando algum estudo vascular e realizado previamente a cirurgia, alem disso, pelo quadro clinico variado e afeccoes cronicas que necessitam de tratamento. Palavras-chave: Cirurgia plastica; sindrome de Sturge-Weber; hemangioma; procedimentos cirurgicos vasculares Introduccion: El Sindrome de Sturge-Weber (SSW) es una afeccion ne