Prenatal diagnosis and postnatal course in four fetuses with very rare pulmonary artery anomalies /Cok nadir gorulen pulmoner arter anomalilerinin prenatal tanisi ve postnatal seyri

Pulmonary artery (PA) anomalies are very rare congenital cardiac malformations, a significant number of which remain unrecognized or misdiagnosed during the prenatal period. We report the prenatal diagnosis and outcome of pregnancy with fetal PA anomalies and discuss the related management issues. We identified four cases of prenatally diagnosed rare PA anomalies that were seen and confirmed in the newborn period by echocardiography and computed tomographic angiography at our center from 2018 to 2020. The course of the pregnancy, perinatal outcome, and the postnatal course in each case were analyzed. Three fetuses were born by repeat cesarean section approximately at 39 weeks of gestation and the other woman delivered vaginally. Of the abnormal origin of the left PA (LPA) in two patients, the first had right PA abnormalities derivating from the ascending aorta, and in the second, the LPA originated from the right PA. Two patients had agenesis of ductus arteriosus (DA), the first was accompanied with tetralogy of Fallot (TOF) and right aortic arch with a normal pulmonary valve, the second patient presented with an Absent Pulmonary Valve syndrome with TOF. Prenatal ultrasonography can be used to correctly diagnose the abnormal origin of the PA branches. Branching of the PA, presence of DA, location of the aortic, and ductal arch by the trachea should be routinely screened in the prenatal anatomic examination and the three-vessel and trachea view can determine the primary clues of PA malformations. Keywords: Agenesis of ductus arteriosus, LPA originating from the ascending aorta, Absent Pulmonary Valve syndrome, LPA sling, right aortic arch, tetralogy of Fallot Pulmoner arter anomalileri cok nadir gorulen konjenital kalp hastaliklarindan olup bircogu prenatal donemde farkedilmeyebilir veya yanlis tanimlanabilmektedir. Burada fetal pulmoner arter anomalilerinin prenatal tanisi ve sonuclarini ve yonetimini tartismayi amacladik. 2018 ile 2020 arasinda klinigimize basvuran prenatal donemde tani konulan dort olgu tanimladik ve postnatal yenidogan doneminde ekokardiyografi ve bilgisayarli tomografik anjiyografi ile tanilarimizi dogruladik. Her olgunun gebelik seyrini, perinatal sonuclarini ve postnatal takiplerini analize ettik. Sezaryan oykusu olan 3 hasta 39. gebelik haftasinda sezaryen ile, 1 hasta normal vajinal yolla dogurtuldu. Olgularin ikisinde sol pulmoner arter anormal orjinli olup bu olgularin ilkinde sol pulmoner arter asendan aortadan cikarken, ikinci