Adrenocortical carcinoma in a 6-month-old infant

Adrenocortical carcinoma (ACC) is a rare malignant tumor arising from the adrenal cortex and it is even rarer in infancy. These tumors are usually hormonally active. We report a case of ACC in a 6-month-old infant who was brought by her mother with complaints of hirsutism and abnormally looking geni...

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Veröffentlicht in:Journal of Indian Association of Pediatric Surgeons 2020-09, Vol.25 (5), p.310-313
Hauptverfasser: Rahar, Seema, Chauhan, Devender, Singh, Shashikant, Ahuja, Arvind, Bhardwaj, Minakshi, Sen, Amita
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Sprache:eng
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Zusammenfassung:Adrenocortical carcinoma (ACC) is a rare malignant tumor arising from the adrenal cortex and it is even rarer in infancy. These tumors are usually hormonally active. We report a case of ACC in a 6-month-old infant who was brought by her mother with complaints of hirsutism and abnormally looking genitalia. Serum 17-alpha-hydroxyprogesterone and serum cortisol levels were raised. Subsequently, imaging studies revealed a large well-circumscribed soft-tissue mass in the right suprarenal region. The tumor was excised, and on histopathology in conjunction with immunohistochemistry, a diagnosis of ACC was given. Only four other cases of ACC have been reported till date in the literature, with an age of 6 months or younger. Hereby, we present a case of ACC in a young infant.
ISSN:0971-9261
1998-3891
DOI:10.4103/jiaps.JIAPS_155_19