Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease : Report of a Case with a 9-Year Follow-Up

Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD). We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD. End-stage chronic...

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Veröffentlicht in:Case reports in gastrointestinal medicine 2014-01, Vol.2014 (2014), p.1-4
Hauptverfasser: Duca, Ileana, Ramírez de la Piscina, Patricia, Estrada, Silvia, Calderón, Rosario, Ganchegui, Idoia, Campos, Amaia, Spicakova, Katerina, Urtasun, Leire, Salvador, Marta, Delgado, Elvira, Bengoa, Raquel, García-Campos, Francisco
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Sprache:eng
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Zusammenfassung:Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD). We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD. End-stage chronic renal failure with a secondary Budd-Chiari syndrome developed during the patient’s clinical course. She underwent combined liver and kidney transplantation, with a successful response over a 9-year follow-up period.
ISSN:2090-6528
2090-6536
DOI:10.1155/2014/585291