Surgical Treatment of Arrhythmogenic Right Ventricular Cardiomyopathy with Absent Pulmonary Valve

Fatty infiltration of right ventricle free wall and absent of pulmonary valve were detected during the operation and only inferior-posterior wall contained a little myocardial fiber [Figure 1]c,[Figure 1]d,[Figure 1]e. In the situation with intact pulmonary annulus, three leaflets were reconstructed independently using autologous pericardium treated with 0.6% glutaraldehyde solution for 10 min [Figure 1]f. For the frequent episodes of syncope, the patient underwent implantation of a biventricular defibrillator. The patients with unexplained syncope, non-sustained...