Dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management

Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplanta...

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Veröffentlicht in:Indian journal of anaesthesia 2015-05, Vol.59 (5), p.312-314
Hauptverfasser: Singh, Anshuman, Pandey, V K, Tandon, Manish, Pandey, C K
Format: Artikel
Sprache:eng
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Zusammenfassung:Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.
ISSN:0019-5049
0976-2817
DOI:10.4103/0019-5049.156888