Clinical observation of a patient with thrombotic thrombocytopenic purpura with renal and intestinal lesions
The article presents a brief description of a rare disease - thrombotic thrombocytopenic purpura (Moshkovits - disease), which is based on the deficiency of ADAMTS-13 metalloproteinase, leading to the development of thrombotic microangiopathy with the defeat of vital organs. The article also describ...
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Veröffentlicht in: | Terapevtic̆eskii arhiv 2019-07, Vol.91 (7), p.106-110 |
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Hauptverfasser: | , , , |
Format: | Artikel |
Sprache: | eng ; rus |
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Online-Zugang: | Volltext |
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Zusammenfassung: | The article presents a brief description of a rare disease - thrombotic thrombocytopenic purpura (Moshkovits - disease), which is based on the deficiency of ADAMTS-13 metalloproteinase, leading to the development of thrombotic microangiopathy with the defeat of vital organs. The article also describes the clinical observation of a patient with the Moshkovits - disease. The features of the above observation are involvement in the pathological process of the kidneys and intestines, while in the classical descriptions of the disease there is a predominant lesion of the Central nervous system, as well as the genetic form of the disease. |
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ISSN: | 0040-3660 2309-5342 |
DOI: | 10.26442/00403660.2019.07.000131 |