Hepatoid carcinoma of the ovary – A case report and literature review

•We have compiled the reported cases of HCO since 1987, having 39 cases including our report.•It is an extremely rare case report.•To make a diagnosis it is necessary a pathologist specializing in gynecology oncology.•All previous reports had radical open surgery, this is the first report of conservative and laparoscopic surgery. We present the case of a 27-year old female with an ovarian tumor and alpha-fetoprotein (AFP) of 1210 ng/m, a right salpingo-oophorectomy was performed and had conservative complementary staging by gynecologic oncologists. The histopathological report was primary hepatoid carcinoma of the ovary (HCO), clinical stage IA, complementary treatment was adjuvant chemotherapy with BEP and remains clinical, imaging and biochemically disease free in three years follow up.