Giant Congenital Melanocytic Nevus with Occipital Encephalocele: A Very Rare Association

A 5-month-old male child with uneventful ante and postnatal history presented with an extensive pigmented growth involving the scalp, left side of the face, neck, upper trunk, and left shoulder with multiple satellite lesions. {Figure 1}{Figure 2}{Figure 3} A computerized tomography (CT) scan of the large scalp mass demonstrated an encephalocele with evidence of herniation of very thin looking redundant brain tissue into the sac.