Reno-appendiceal fistula in autosomal dominant polycystic kidney disease

We present a very rare Case of a 53-year-old female with autosomal dominant polycystic kidney disease (ADPKD) who was incidentally found to have a reno-appendiceal fistula while undergoing open bilateral nephrectomy. The mid-portion of the appendix was fistulized to a cyst in the lower pole of the right kidney. The etiology was likely due to chronic inflammation. An appendectomy was performed along with the planned right nephrectomy to ensure complete removal of the fistulous tract. •The development of a fistulous communication between the kidney and intestinal tract is a rare event.•These fistulas are usually a consequence of chronic, inflammatory disease of the urinary or gastrointestinal tract.•There has never been a report of a reno-appendiceal fistula in a patient with ADPKD.