Chinese expert consensus statement on the diagnosis and treatment of Hirschsprung disease

The current consensus statement is aimed at standardizing the diagnostic and surgical strategies, and emphasizing postoperative rehabilitation training, to systematically improve postoperative recovery and to improve the quality of life in long-term follow-up. In a systematic review, CE had a mean sensitivity of 70% (95% confidence interval [CI]: 64–76%) and a mean specificity of 83% (95% CI: 74–90%) for the diagnosis of HSCR. (Grade 2D) Surgery for HSCR Compared with multistage surgery, the single-stage pull-through procedure has the prominent advantages of shortening the length of hospital stay, reducing the number of operations, decreasing hospitalization costs, and avoiding complications of enterostomy. European Reference Network for rare Inherited and Congenital Anomalies (ERNICA) guidelines recommended preoperative saline rectal irrigation to overcome functional bowel obstruction and to enable enteral feeding.