Ectopic intra-scrotal supernumerary kidney

Supernumerary kidney is a rare congenital urologic malformation, of which approximately a hundred cases exist to date in the literature. This anomaly is an accessory kidney that possesses its own collecting system, blood supply and encapsulated parenchyma. We report the case of an eleven-month-old male infant presenting with multiple urinary tract infections and a dilated left ectopic ureter with grade II vesicoureteral reflux. The diagnosis of ectopic intra-scrotal supernumerary kidney was evoked following MRI, scrotal ultrasound and endoscopic exploration. Surgical resection by laparoscopy was subsequently performed and the postoperative course was uneventful. Supernumerary kidney is an extremely rare urologic malformation that requires multimodal preoperative imaging and management in a specialized pediatric surgical facility.