Dermatofibrosarcoma Protuberans of Scalp - An Unusual Site of Occurrence

In Immunohistochemistry [IHC], the sections showed positivity for S100, Ki67, and negative for CD34, and a final confirmatory diagnosis of low-grade spindle cell sarcoma was made. Since the lesion was diagnosed as DFSP, the margin status ought to be confirmed. [...]a re-excision of margins was performed and they were reported to be negative for malignancy. The radiography of the present case there was no cranial involvement nor was there any metastasis noted. Since dermoid cyst was the clinical diagnosis made, the need for MRI was not anticipated. [...]the literature says that MRIs cannot be relied on in such cases as they may not always distinguish DFSPs from other soft tissue sarcomas. [...]we should be aware of this uncommon entity and always perform a wide excision for these tumors to reduce the risk of recurrence.