Arrhythmias and cardiac MRI associations in patients with established cardiac dystrophinopathy

AimsSome patients with cardiac dystrophinopathy die suddenly. Whether such deaths are preventable by specific antiarrhythmic management or simply indicate heart failure overwhelming medical therapies is uncertain. The aim of this prospective, cohort study was to describe the occurrence and nature of cardiac arrhythmias recorded during prolonged continuous ECG rhythm surveillance in patients with established cardiac dystrophinopathy and relate them to abnormalities on cardiac MRI.Methods and resultsA cohort of 10 patients (36.3 years; 3 female) with LVEF