Case for diagnosis. Systemic light chain amyloidosis with cutaneous involvement

Systemic light chain amiloydosis is a rare disease. Due to its typical cutaneous lesions, dermatologists play an essential role in its diagnosis. Clinical manifestations vary according to the affected organ and are often unspecific. Definitive diagnosis is achieved through biopsy. We report a patien...

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Veröffentlicht in:Anais brasileiros de dermatología 2017-10, Vol.92 (5), p.731-732
Hauptverfasser: Gontijo, João Renato Vianna, Pinto, Jackson Machado, Paula, Maysa Carla de
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Sprache:eng
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Zusammenfassung:Systemic light chain amiloydosis is a rare disease. Due to its typical cutaneous lesions, dermatologists play an essential role in its diagnosis. Clinical manifestations vary according to the affected organ and are often unspecific. Definitive diagnosis is achieved through biopsy. We report a patient with palpebral amyloidosis, typical bilateral ecchymoses and cardiac involvement, without plasma cell dyscrasia or lymphomas. The patient died shortly after the diagnosis.
ISSN:0365-0596
1806-4841
1806-4841
0365-0596
DOI:10.1590/abd1806-4841.20176958