Budd-Chiari Syndrome: An Unusual Complication of AL Amyloidosis

Budd-Chiari syndrome (BCS) is an uncommon congestive hepatopathy caused by blockage of hepatic veins in the absence of cardiac/pericardial disorders as well as hepatic veno-occlusive disease [1]. In 75% of patients with BCS there is an underlying condition that predisposes to blood clotting [2]. More than one etiological factor may play a role in 25% of cases [2]. Coagulation problems mainly involving bleeding abnormalities are well recognized in AL amyloidosis while thrombosis is a less common feature [3]. Here, we report a rare case of AL amyloidosis complicated by BCS.