Transumbilical laparoscopic treatment of Congenital Infantile Fibrosarcoma of the Ileum

Transumbilical laparoscopic treatment of Congenital Infantile Fibrosarcoma of the Ileum

Congenital-Infantile Fibrosarcoma (CIF) is a malignant mesenchymal tumor representing 10-20% of soft-tissue tumors. Complete surgical resection is generally the treatment of choice. The most recurrent cytogenetic abnormality was identified as the traslocation t(12;15)(p13:q25), which bears the fusio...

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Veröffentlicht in:La Pediatria medica e chirurgica 2014-08, Vol.36 (4), p.93-93
Hauptverfasser: Scirè, G, Mantovani, A, Zampieri, N, Guerriero, V A, Segala, D, Pecori, S, Bruno, C, Camoglio, F S
Format: Artikel
Sprache:eng
Schlagworte:
Congenital Fibrosarcoma
Female
Fibrosarcoma - congenital
Fibrosarcoma - genetics
Fibrosarcoma - surgery
genetic translocation
Humans
Ileum - pathology
Infant, Newborn
intestinal neonatal occlusion
Intestinal Obstruction - etiology
Intestinal Obstruction - surgery
laparoscopic treatment
Laparoscopy - methods
Soft Tissue Neoplasms - congenital
Soft Tissue Neoplasms - genetics
Soft Tissue Neoplasms - surgery
Umbilicus
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Zusammenfassung:Congenital-Infantile Fibrosarcoma (CIF) is a malignant mesenchymal tumor representing 10-20% of soft-tissue tumors. Complete surgical resection is generally the treatment of choice. The most recurrent cytogenetic abnormality was identified as the traslocation t(12;15)(p13:q25), which bears the fusion of Tel gene EVT6 with TrkC gene. This study describes a case of infantile fibrosarcoma of the ileum in a female newborn examined for intestinal occlusion and its laparoscopic treatment.
ISSN:0391-5387
2420-7748
DOI:10.4081/pmc.2014.93