Bilateral pneumothoraces with apical consolidations

Bilateral pneumothoraces are extremely rare. Patients with pleuroparenchymal fibroelastosis are frequently complicated by pneumothorax, which is sometimes bilateral. Pleuroparenchymal fibroelastosis should be considered a cause of bilateral pneumothoraces with apical fibrosis. Bilateral pneumothoraces are extremely rare. We present a fatal case of a patient diagnosed with secondary pneumothorax associated with idiopathic pleuroparenchymal fibroelastosis (PPFE) who died of type II respiratory failure one year after the onset of pneumothorax. PPFE should be considered a cause of bilateral pneumothoraces with apical fibrosis.