Vaginoplasty with Uterovaginal Anastomosis for partial Vaginal and Complete Cervical Agenesis: A Rare Müllerian Anomaly

Congenital absence of cervix is a rare condition that occurs in 1 in 80,000 to 100,000 births. Here, we report a case of a 20-year-old, married woman who presented to the gynecology outpatient department with primary amenorrhea and complaints of cyclical left-sided lower abdominal pain and difficult coitus for 2 years. Magnetic resonance imaging report suggested unicornuate uterus with hematometra and cervical agenesis. On laparotomy, unicornuate globular uterine horn with absent cervix was present on the left side and separate solid rudimentary horn was found on right lateral pelvic wall. Left adnexa was normal, whereas right ovary was enlarged with minimal hydrosalpinx. Vaginoplasty with uterovaginal anastomosis was performed after draining the hematometra and successful restoration of cyclical menses was achieved on follow-up.