A Case of a Coronary Arteriovenous Fistula Associated with a Right Single Coronary Artery

A 3-year-old girl was given a diagnosis of coronary arteriovenous fistula associated with a single right coronary artery on cardiac catheterization. The left coronary artery arose from the proximal part of the right coronary artery. The dilated left coronary artery ran in front of the right ventricular outflow tract and then divided into the left anterior descending branch and the left circumflex artery. A coronary arteriovenous fistula was in the left main coronary artery and opened into the right ventricular outflow tract. Under cardiopulmonary bypass and cardiac arrest, a transverse incision was made at the right ventricular outflow tract 1cm below the dilated vessel and the 5-mm oval-shaped orifice of the fistula was identified. This fistula was closed with a pledgetted mattress suture reinforced with over-and-over suture. Catheterization 8 months after surgery demonstrated no residual shunt and she has been doing well.