A rare variant of scalp dermatofibrosarcoma protuberans: malignant fibrous histiocytomatous transformation

Dermatofibrosarcoma protuberans (DFSP) is a relatively uncommon, local aggressive tumor. Tumor metastasis is rare, and it has equal sex distribution. DFSP usually develops on the trunk and extremities. Scalp DFSP composes less than 5% of all cases. Local recurrence rates are high. Wide local excision and Mohs surgery are options for treatment. Fibrosarcomatous or malignant fibrous histiocytomatous transformation of DFSP are rare conditions. In this article, we described a case of a giant DFSP over the scalp containing malignant fibrous histiocytomatous transformation areas.