Clinical profiles of pulmonary lymphangioleiomyomatosis in the mainland of China

Pulmonary lymphangioleiomyomatosis (PLAM) is a rare disease primarily occurring in women at reproductive age, and characterized by abnormal proliferation of immature smooth muscle cells named lymphangioleiomyomatosis (LAM) cells in the pulmonary lymphatics, blood vessels and airways, resulting in re...

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Veröffentlicht in:Chinese medical journal 2009-06, Vol.122 (12), p.1473-1476
Hauptverfasser: Xu, Feng, Yang, Yan, Xia, Jing-Yan, Chen, Xi-Yuan, Wang, Hui-Ying, Shen, Hua-Hao
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container_end_page 1476
container_issue 12
container_start_page 1473
container_title Chinese medical journal
container_volume 122
creator Xu, Feng
Yang, Yan
Xia, Jing-Yan
Chen, Xi-Yuan
Wang, Hui-Ying
Shen, Hua-Hao
description Pulmonary lymphangioleiomyomatosis (PLAM) is a rare disease primarily occurring in women at reproductive age, and characterized by abnormal proliferation of immature smooth muscle cells named lymphangioleiomyomatosis (LAM) cells in the pulmonary lymphatics, blood vessels and airways, resulting in respiratory failure and death.
doi_str_mv 10.3760/cma.j.issn.0366-6999.2009.12.023
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source MEDLINE; DOAJ Directory of Open Access Journals; EZB-FREE-00999 freely available EZB journals
subjects Adolescent
Adult
Aged
China
Female
Humans
Lymphangioleiomyomatosis - diagnosis
Lymphangioleiomyomatosis - diagnostic imaging
Lymphangioleiomyomatosis - drug therapy
Lymphangioleiomyomatosis - therapy
Male
Middle Aged
PLAM
Radiography
Respiratory Function Tests
Young Adult
临床概况
平滑肌细胞
异常增殖
育龄妇女
肺淋巴管平滑肌瘤病
title Clinical profiles of pulmonary lymphangioleiomyomatosis in the mainland of China
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