职业粉尘暴露相关PAP 1例并文献复习

R563; 肺泡蛋白沉积症(pulmonary alveolar proteinosis,PAP)是一类呼吸系统罕见疾病,以肺泡腔及终末呼吸性细支气管内表面活性物质组分沉积为主要特征.职业粉尘暴露相关的PAP报道较少,预后差.本文将结合1例病例,分别对其临床特点、影像学改变、病理特征及治疗预后进行分析,并结合文献复习....

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Veröffentlicht in:医学信息 2017, Vol.30 (16), p.190-191
Hauptverfasser: 杨立春, 贺航咏
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贺航咏
description R563; 肺泡蛋白沉积症(pulmonary alveolar proteinosis,PAP)是一类呼吸系统罕见疾病,以肺泡腔及终末呼吸性细支气管内表面活性物质组分沉积为主要特征.职业粉尘暴露相关的PAP报道较少,预后差.本文将结合1例病例,分别对其临床特点、影像学改变、病理特征及治疗预后进行分析,并结合文献复习.
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title 职业粉尘暴露相关PAP 1例并文献复习
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