Primary desmoplastic small round cell tumor of the duodenum

The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray re...

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Veröffentlicht in:European journal of medical research 2014-07, Vol.19 (1), p.38-38, Article 38
Hauptverfasser: Liu, Qi, Liu, Nan, Chen, DeXing
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Liu, Nan
Chen, DeXing
description The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.
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A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. 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source MEDLINE; DOAJ Directory of Open Access Journals; SpringerLink Journals; Elektronische Zeitschriftenbibliothek - Frei zugängliche E-Journals; PubMed Central Open Access; Springer Nature OA Free Journals; PubMed Central
subjects Adolescent
Antineoplastic Combined Chemotherapy Protocols - administration & dosage
Cancer
Care and treatment
Case Report
Case studies
Chemotherapy, Adjuvant
Desmoplastic Small Round Cell Tumor - diagnostic imaging
Desmoplastic Small Round Cell Tumor - drug therapy
Desmoplastic Small Round Cell Tumor - pathology
Diagnosis
Duodenal Neoplasms - diagnostic imaging
Duodenal Neoplasms - drug therapy
Duodenal Neoplasms - pathology
Duodenum - pathology
Duodenum - surgery
Female
Health aspects
Humans
Metastasis
Teenage girls
Tomography, X-Ray Computed
Ultrasonography
title Primary desmoplastic small round cell tumor of the duodenum
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