Primary desmoplastic small round cell tumor of the duodenum
The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray re...
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Veröffentlicht in: | European journal of medical research 2014-07, Vol.19 (1), p.38-38, Article 38 |
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description | The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease. |
doi_str_mv | 10.1186/2047-783X-19-38 |
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A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.</description><identifier>ISSN: 2047-783X</identifier><identifier>ISSN: 0949-2321</identifier><identifier>EISSN: 2047-783X</identifier><identifier>DOI: 10.1186/2047-783X-19-38</identifier><identifier>PMID: 24997683</identifier><language>eng</language><publisher>England: BioMed Central Ltd</publisher><subject>Adolescent ; Antineoplastic Combined Chemotherapy Protocols - administration & dosage ; Cancer ; Care and treatment ; Case Report ; Case studies ; Chemotherapy, Adjuvant ; Desmoplastic Small Round Cell Tumor - diagnostic imaging ; Desmoplastic Small Round Cell Tumor - drug therapy ; Desmoplastic Small Round Cell Tumor - pathology ; Diagnosis ; Duodenal Neoplasms - diagnostic imaging ; Duodenal Neoplasms - drug therapy ; Duodenal Neoplasms - pathology ; Duodenum - pathology ; Duodenum - surgery ; Female ; Health aspects ; Humans ; Metastasis ; Teenage girls ; Tomography, X-Ray Computed ; Ultrasonography</subject><ispartof>European journal of medical research, 2014-07, Vol.19 (1), p.38-38, Article 38</ispartof><rights>COPYRIGHT 2014 BioMed Central Ltd.</rights><rights>Copyright © 2014 Liu et al.; licensee BioMed Central Ltd. 2014 Liu et al.; licensee BioMed Central Ltd.</rights><lds50>peer_reviewed</lds50><oa>free_for_read</oa><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-b550t-c286c88c1324954264e8fc7110a37baded90ceaa9c3bc6b9441989c1476313b73</citedby><cites>FETCH-LOGICAL-b550t-c286c88c1324954264e8fc7110a37baded90ceaa9c3bc6b9441989c1476313b73</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktopdf>$$Uhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC4096735/pdf/$$EPDF$$P50$$Gpubmedcentral$$Hfree_for_read</linktopdf><linktohtml>$$Uhttps://www.ncbi.nlm.nih.gov/pmc/articles/PMC4096735/$$EHTML$$P50$$Gpubmedcentral$$Hfree_for_read</linktohtml><link.rule.ids>230,314,727,780,784,864,885,27924,27925,53791,53793</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/24997683$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Liu, Qi</creatorcontrib><creatorcontrib>Liu, Nan</creatorcontrib><creatorcontrib>Chen, DeXing</creatorcontrib><title>Primary desmoplastic small round cell tumor of the duodenum</title><title>European journal of medical research</title><addtitle>Eur J Med Res</addtitle><description>The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.</description><subject>Adolescent</subject><subject>Antineoplastic Combined Chemotherapy Protocols - administration & dosage</subject><subject>Cancer</subject><subject>Care and treatment</subject><subject>Case Report</subject><subject>Case studies</subject><subject>Chemotherapy, Adjuvant</subject><subject>Desmoplastic Small Round Cell Tumor - diagnostic imaging</subject><subject>Desmoplastic Small Round Cell Tumor - drug therapy</subject><subject>Desmoplastic Small Round Cell Tumor - pathology</subject><subject>Diagnosis</subject><subject>Duodenal Neoplasms - diagnostic imaging</subject><subject>Duodenal Neoplasms - drug therapy</subject><subject>Duodenal Neoplasms - pathology</subject><subject>Duodenum - pathology</subject><subject>Duodenum - surgery</subject><subject>Female</subject><subject>Health aspects</subject><subject>Humans</subject><subject>Metastasis</subject><subject>Teenage girls</subject><subject>Tomography, X-Ray Computed</subject><subject>Ultrasonography</subject><issn>2047-783X</issn><issn>0949-2321</issn><issn>2047-783X</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2014</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNp1kk1LxDAQhoMoKurZmxQE8VJtmjQfCIKKXyDoQcFbSNOpG2matWkF_70p1WUXNDlkmHnmzcwwCO3j7ARjwU7zjPKUC_KaYpkSsYa2F571JXsL7YXwnsXDcsal3ERbOZWSM0G20dlTZ53uvpIKgvPzRofemiQ43TRJ54e2SgxEsx-c7xJfJ_0MkmrwFbSD20UbtW4C7P28O-jl5vr56i59eLy9v7p4SMuiyPrU5IIZIQwm8duC5oyCqA3HONOEl7qCSmYGtJaGlIaVklIshTSYckYwKTnZQeeT7nwoHVQG2r7TjZpPlSuvrVqNtHam3vynoplknBRR4HISKK3_R2A1YrxT4_zUOD-FpSIiihz_VNH5jwFCr5wN43B0C34IChc0NkcIH9HDCX3TDSjb1j6qmhFXFwXFecEwG6mTP6h4K3DW-BZqG_0rCUdLCTPQTT8Lvhl669uwCp5OoOl8CB3Ui1ZxpsbV-aO5g-URL_jfRSHfq4m9rA</recordid><startdate>20140706</startdate><enddate>20140706</enddate><creator>Liu, Qi</creator><creator>Liu, Nan</creator><creator>Chen, DeXing</creator><general>BioMed Central Ltd</general><general>BioMed Central</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope><scope>5PM</scope></search><sort><creationdate>20140706</creationdate><title>Primary desmoplastic small round cell tumor of the duodenum</title><author>Liu, Qi ; Liu, Nan ; Chen, DeXing</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-b550t-c286c88c1324954264e8fc7110a37baded90ceaa9c3bc6b9441989c1476313b73</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2014</creationdate><topic>Adolescent</topic><topic>Antineoplastic Combined Chemotherapy Protocols - administration & dosage</topic><topic>Cancer</topic><topic>Care and treatment</topic><topic>Case Report</topic><topic>Case studies</topic><topic>Chemotherapy, Adjuvant</topic><topic>Desmoplastic Small Round Cell Tumor - diagnostic imaging</topic><topic>Desmoplastic Small Round Cell Tumor - drug therapy</topic><topic>Desmoplastic Small Round Cell Tumor - pathology</topic><topic>Diagnosis</topic><topic>Duodenal Neoplasms - diagnostic imaging</topic><topic>Duodenal Neoplasms - drug therapy</topic><topic>Duodenal Neoplasms - pathology</topic><topic>Duodenum - pathology</topic><topic>Duodenum - surgery</topic><topic>Female</topic><topic>Health aspects</topic><topic>Humans</topic><topic>Metastasis</topic><topic>Teenage girls</topic><topic>Tomography, X-Ray Computed</topic><topic>Ultrasonography</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Liu, Qi</creatorcontrib><creatorcontrib>Liu, Nan</creatorcontrib><creatorcontrib>Chen, DeXing</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><collection>PubMed Central (Full Participant titles)</collection><jtitle>European journal of medical research</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Liu, Qi</au><au>Liu, Nan</au><au>Chen, DeXing</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Primary desmoplastic small round cell tumor of the duodenum</atitle><jtitle>European journal of medical research</jtitle><addtitle>Eur J Med Res</addtitle><date>2014-07-06</date><risdate>2014</risdate><volume>19</volume><issue>1</issue><spage>38</spage><epage>38</epage><pages>38-38</pages><artnum>38</artnum><issn>2047-783X</issn><issn>0949-2321</issn><eissn>2047-783X</eissn><abstract>The desmoplastic small round cell tumor (DSRCT) is an extremely rare tumor that mainly affects adolescents and mostly involves the abdominal and pelvic peritoneum. A 14-year-old girl presented with intermittent epigastric pain; abdominal computed tomography and upper gastrointestinal barium X-ray revealed an 8 cm × 10 cm space-occupying mass in the duodenal region. The patient underwent pancreaticoduodenectomy and the final pathologic diagnosis was DSRCT. Although multi-agent systemic chemotherapy was given, the patient died of metastasis 8 months later. Early diagnosis and surgical treatment with adjuvant chemotherapy seems to be the best treatment choice for this disease.</abstract><cop>England</cop><pub>BioMed Central Ltd</pub><pmid>24997683</pmid><doi>10.1186/2047-783X-19-38</doi><tpages>1</tpages><oa>free_for_read</oa></addata></record> |
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subjects | Adolescent Antineoplastic Combined Chemotherapy Protocols - administration & dosage Cancer Care and treatment Case Report Case studies Chemotherapy, Adjuvant Desmoplastic Small Round Cell Tumor - diagnostic imaging Desmoplastic Small Round Cell Tumor - drug therapy Desmoplastic Small Round Cell Tumor - pathology Diagnosis Duodenal Neoplasms - diagnostic imaging Duodenal Neoplasms - drug therapy Duodenal Neoplasms - pathology Duodenum - pathology Duodenum - surgery Female Health aspects Humans Metastasis Teenage girls Tomography, X-Ray Computed Ultrasonography |
title | Primary desmoplastic small round cell tumor of the duodenum |
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