Weber-Christian disease presenting with proptosis: a case report
Weber-Christian disease (WCD) is a rare inflammatory disease of adipose tissue, which is characterized by painful cutaneous nodules and constitutional symptoms. Although any area of the body containing fat can be affected by WCD, the involvement of retrobulbar fat is uncommon and proptosis is a rare...
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| Veröffentlicht in: | Journal of Korean medical science 2000-04, Vol.15 (2), p.247-250 |
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| creator | Hyun, S H Kang, Y M Kim, C D Lee, J M Kim, I T Kim, N S |
| description | Weber-Christian disease (WCD) is a rare inflammatory disease of adipose tissue, which is characterized by painful cutaneous nodules and constitutional symptoms. Although any area of the body containing fat can be affected by WCD, the involvement of retrobulbar fat is uncommon and proptosis is a rare presenting manifestation. We report a case who presented with proptosis of the right eye which is accompanied by painful subcutaneous nodules, high fever and myalgia. Biopsies of retrobulbar tissue and suprapubic nodule showed lobular panniculitis with mixed cellular infiltration, mainly composed of histiocytes and lymphocytes. He responded well to high-dose glucocorticoid. |
| doi_str_mv | 10.3346/jkms.2000.15.2.247 |
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He responded well to high-dose glucocorticoid.</description><subject>Adult</subject><subject>Biopsy</subject><subject>Exophthalmos - drug therapy</subject><subject>Exophthalmos - etiology</subject><subject>Exophthalmos - pathology</subject><subject>Glucocorticoids - administration & dosage</subject><subject>Humans</subject><subject>Magnetic Resonance Imaging</subject><subject>Male</subject><subject>Panniculitis, Nodular Nonsuppurative - complications</subject><subject>Panniculitis, Nodular Nonsuppurative - drug therapy</subject><subject>Panniculitis, Nodular Nonsuppurative - pathology</subject><issn>1011-8934</issn><issn>1598-6357</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2000</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNpVkMtOwzAQRS0EoqXwAyxQVuwS_LbDAoEqXlIlNiCWlpPYrUte2CmIv8dRK1RWM6O5c-fqAHCOYEYI5VfrjyZkGEKYIZbhDFNxAKaI5TLlhInD2EOEUpkTOgEnIawhxIxhcgwmCEpIBBRTcPtuCuPT-cq7MDjdJpULRgeT9N4E0w6uXSbfbljFueuHLrhwneikHBXe9J0fTsGR1XUwZ7s6A28P96_zp3Tx8vg8v1ukJcnlkHJpCTU5hYIWlbQY8Sq3zAorjSBFWVBjcQG11BUvbU4ILrTAsqKECwkxF2QGbra-_aZoTFXGbF7Xqveu0f5Hddqp_5vWrdSy-1IEMsoRiQaXOwPffW5MGFTjQmnqWrem2wQlIpQcMRqFeCssfReCN_bvCYJqBK9G8GoErxBTWEXw8ehiP97eyZY0-QUFRIFD</recordid><startdate>20000401</startdate><enddate>20000401</enddate><creator>Hyun, S H</creator><creator>Kang, Y M</creator><creator>Kim, C D</creator><creator>Lee, J M</creator><creator>Kim, I T</creator><creator>Kim, N S</creator><general>Korean Academy of Medical Sciences</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope><scope>5PM</scope></search><sort><creationdate>20000401</creationdate><title>Weber-Christian disease presenting with proptosis: a case report</title><author>Hyun, S H ; Kang, Y M ; Kim, C D ; Lee, J M ; Kim, I T ; Kim, N S</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c398t-68f34e94074bd8f216d9f5f7f8e73bcb4ef2b0a8ad6cf9332ba728d4367802673</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2000</creationdate><topic>Adult</topic><topic>Biopsy</topic><topic>Exophthalmos - drug therapy</topic><topic>Exophthalmos - etiology</topic><topic>Exophthalmos - pathology</topic><topic>Glucocorticoids - administration & dosage</topic><topic>Humans</topic><topic>Magnetic Resonance Imaging</topic><topic>Male</topic><topic>Panniculitis, Nodular Nonsuppurative - complications</topic><topic>Panniculitis, Nodular Nonsuppurative - drug therapy</topic><topic>Panniculitis, Nodular Nonsuppurative - pathology</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Hyun, S H</creatorcontrib><creatorcontrib>Kang, Y M</creatorcontrib><creatorcontrib>Kim, C D</creatorcontrib><creatorcontrib>Lee, J M</creatorcontrib><creatorcontrib>Kim, I T</creatorcontrib><creatorcontrib>Kim, N S</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><collection>PubMed Central (Full Participant titles)</collection><jtitle>Journal of Korean medical science</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Hyun, S H</au><au>Kang, Y M</au><au>Kim, C D</au><au>Lee, J M</au><au>Kim, I T</au><au>Kim, N S</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Weber-Christian disease presenting with proptosis: a case report</atitle><jtitle>Journal of Korean medical science</jtitle><addtitle>J Korean Med Sci</addtitle><date>2000-04-01</date><risdate>2000</risdate><volume>15</volume><issue>2</issue><spage>247</spage><epage>250</epage><pages>247-250</pages><issn>1011-8934</issn><eissn>1598-6357</eissn><abstract>Weber-Christian disease (WCD) is a rare inflammatory disease of adipose tissue, which is characterized by painful cutaneous nodules and constitutional symptoms. Although any area of the body containing fat can be affected by WCD, the involvement of retrobulbar fat is uncommon and proptosis is a rare presenting manifestation. We report a case who presented with proptosis of the right eye which is accompanied by painful subcutaneous nodules, high fever and myalgia. Biopsies of retrobulbar tissue and suprapubic nodule showed lobular panniculitis with mixed cellular infiltration, mainly composed of histiocytes and lymphocytes. He responded well to high-dose glucocorticoid.</abstract><cop>Korea (South)</cop><pub>Korean Academy of Medical Sciences</pub><pmid>10803707</pmid><doi>10.3346/jkms.2000.15.2.247</doi><tpages>4</tpages><oa>free_for_read</oa></addata></record> |
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| source | MEDLINE; KoreaMed Open Access; EZB-FREE-00999 freely available EZB journals; PubMed Central; PubMed Central Open Access |
| subjects | Adult Biopsy Exophthalmos - drug therapy Exophthalmos - etiology Exophthalmos - pathology Glucocorticoids - administration & dosage Humans Magnetic Resonance Imaging Male Panniculitis, Nodular Nonsuppurative - complications Panniculitis, Nodular Nonsuppurative - drug therapy Panniculitis, Nodular Nonsuppurative - pathology |
| title | Weber-Christian disease presenting with proptosis: a case report |
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