WT1 and PAX-2 Podocyte Expression in Denys-Drash Syndrome and Isolated Diffuse Mesangial Sclerosis

Denys-Drash syndrome is a rare disorder of urogenital development characterized by the association of early onset glomerulopathy caused by diffuse mesangial sclerosis, gonadal dysgenesis leading to pseudohermaphroditism in males, and a high risk of developing Wilms' tumor. The syndrome is cause...

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Veröffentlicht in:	The American journal of pathology 1999, Vol.154 (1), p.181-192
Hauptverfasser:	Yang, Youxin, Jeanpierre, Cécile, Dressler, Gregory R., Lacoste, Mireille, Niaudet, Patrick, Gubler, Marie-Claire
Format:	Artikel
Sprache:	eng
Schlagworte:	Animals Biological and medical sciences Complex syndromes Developmental Disabilities - metabolism Developmental Disabilities - pathology DNA-Binding Proteins - metabolism Female Female Urogenital Diseases - metabolism Female Urogenital Diseases - pathology Fetus Genitalia - abnormalities Genitalia - pathology Glomerular Mesangium - pathology Glomerulosclerosis, Focal Segmental - metabolism Glomerulosclerosis, Focal Segmental - pathology Humans Infant, Newborn Kidney Diseases - metabolism Kidney Diseases - pathology Kidney Glomerulus - pathology Male Male Urogenital Diseases Medical genetics Medical sciences PAX2 Transcription Factor Regular Sclerosis Syndrome Transcription Factors - metabolism WT1 Proteins
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