Renal Failure in Sisters with Cystinuria and the Management of Amino Acids in Chronic Hemodialysis
Two sisters received long-term hemodialysis to manage chronic renal failure resulting from treatment of their cystinuria. Both had progressive renal failure caused by D-penicillamine treatment after surgery for urolithiasis. These are the first reported cases involving sisters. The 34-year-old siste...
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| Veröffentlicht in: | Nihon Jinzo Gakkai shi 1985, Vol.27(3), pp.319-325 |
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| container_issue | 3 |
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| container_title | Nihon Jinzo Gakkai shi |
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| creator | HOSOKAWA, SHINICHI TOMOYOSHI, TADAO KAWAMURA, JUICHI YOSHIDA, OSAMU |
| description | Two sisters received long-term hemodialysis to manage chronic renal failure resulting from treatment of their cystinuria. Both had progressive renal failure caused by D-penicillamine treatment after surgery for urolithiasis. These are the first reported cases involving sisters. The 34-year-old sister had received dialysis since April 1975 and her 26-year-old sister had been on dialysis since October 1977. There has been little variation in the treatment of chronic renal failure whether caused by cystinuria or by other diseases. However, we treated these sisters with cystinuria, along with other patients, by differential diet management. The balance of plasma amino acids improved remarkably after 3.5 years of treatment and both sisters are now undergoing excellent dialysis. The diet restricts methionine and crystine to 2.5 g/day. |
| doi_str_mv | 10.14842/jpnjnephrol1959.27.319 |
| format | Article |
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Both had progressive renal failure caused by D-penicillamine treatment after surgery for urolithiasis. These are the first reported cases involving sisters. The 34-year-old sister had received dialysis since April 1975 and her 26-year-old sister had been on dialysis since October 1977. There has been little variation in the treatment of chronic renal failure whether caused by cystinuria or by other diseases. However, we treated these sisters with cystinuria, along with other patients, by differential diet management. The balance of plasma amino acids improved remarkably after 3.5 years of treatment and both sisters are now undergoing excellent dialysis. 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The diet restricts methionine and crystine to 2.5 g/day.</description><subject>Adult</subject><subject>amino acid treatment</subject><subject>Cystinuria - diet therapy</subject><subject>Cystinuria - drug therapy</subject><subject>Cystinuria - genetics</subject><subject>cystinuria in sisters</subject><subject>Female</subject><subject>hemodialysis</subject><subject>Humans</subject><subject>Kidney Failure, Chronic - chemically induced</subject><subject>Kidney Failure, Chronic - therapy</subject><subject>Penicillamine - adverse effects</subject><subject>Renal Dialysis - methods</subject><subject>renal failure</subject><issn>0385-2385</issn><issn>1884-0728</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1985</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNpdkMtOwzAQRS0EKlXpJyD8Ayl-x1lWFVBEERKPdWTHDnGUOJHtCvXvCWrVBbO4szgzo7kXgDuMVphJRu7b0bfejk0YOlzwYkXyFcXFBZhjKVmGciIvwRxRyTMyyTVYxtiiqUQhGMUzMGOIYFyIOdDv1qsOPirX7YOFzsMPF5MNEf641MDNISbn98EpqLyBqbHwVXn1bXvrExxquO6dH-C6cib-LW-ml7yr4Nb2g3GqO0QXb8BVrbpol6e-AF-PD5-bbbZ7e3rerHdZSzhPmVG1QhUh2hQUi9ogjkjOrOFMWE0lNVqJ2nKEqBBE14QiJAXTOUdSk6owdAFuj3fHve6tKcfgehUO5cnrxF-OvI1pcnDmKiRXdbb8F2pJ8pIeZcr2PFU1KpTW01_wrXYJ</recordid><startdate>1985</startdate><enddate>1985</enddate><creator>HOSOKAWA, SHINICHI</creator><creator>TOMOYOSHI, TADAO</creator><creator>KAWAMURA, JUICHI</creator><creator>YOSHIDA, OSAMU</creator><general>Japanese Society of Nephrology</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope></search><sort><creationdate>1985</creationdate><title>Renal Failure in Sisters with Cystinuria and the Management of Amino Acids in Chronic Hemodialysis</title><author>HOSOKAWA, SHINICHI ; TOMOYOSHI, TADAO ; KAWAMURA, JUICHI ; YOSHIDA, OSAMU</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-j255t-dafa0c22bd9316fd050274ed546eb383dba6fe5003662bf2300864b7508b2c9d3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1985</creationdate><topic>Adult</topic><topic>amino acid treatment</topic><topic>Cystinuria - diet therapy</topic><topic>Cystinuria - drug therapy</topic><topic>Cystinuria - genetics</topic><topic>cystinuria in sisters</topic><topic>Female</topic><topic>hemodialysis</topic><topic>Humans</topic><topic>Kidney Failure, Chronic - chemically induced</topic><topic>Kidney Failure, Chronic - therapy</topic><topic>Penicillamine - adverse effects</topic><topic>Renal Dialysis - methods</topic><topic>renal failure</topic><toplevel>online_resources</toplevel><creatorcontrib>HOSOKAWA, SHINICHI</creatorcontrib><creatorcontrib>TOMOYOSHI, TADAO</creatorcontrib><creatorcontrib>KAWAMURA, JUICHI</creatorcontrib><creatorcontrib>YOSHIDA, OSAMU</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><jtitle>Nihon Jinzo Gakkai shi</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>HOSOKAWA, SHINICHI</au><au>TOMOYOSHI, TADAO</au><au>KAWAMURA, JUICHI</au><au>YOSHIDA, OSAMU</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Renal Failure in Sisters with Cystinuria and the Management of Amino Acids in Chronic Hemodialysis</atitle><jtitle>Nihon Jinzo Gakkai shi</jtitle><addtitle>Jpn J Nephrol</addtitle><date>1985</date><risdate>1985</risdate><volume>27</volume><issue>3</issue><spage>319</spage><epage>325</epage><pages>319-325</pages><issn>0385-2385</issn><eissn>1884-0728</eissn><abstract>Two sisters received long-term hemodialysis to manage chronic renal failure resulting from treatment of their cystinuria. 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| fulltext | fulltext |
| identifier | ISSN: 0385-2385 |
| ispartof | The Japanese Journal of Nephrology, 1985, Vol.27(3), pp.319-325 |
| issn | 0385-2385 1884-0728 |
| language | eng |
| recordid | cdi_pubmed_primary_4021196 |
| source | MEDLINE; EZB-FREE-00999 freely available EZB journals |
| subjects | Adult amino acid treatment Cystinuria - diet therapy Cystinuria - drug therapy Cystinuria - genetics cystinuria in sisters Female hemodialysis Humans Kidney Failure, Chronic - chemically induced Kidney Failure, Chronic - therapy Penicillamine - adverse effects Renal Dialysis - methods renal failure |
| title | Renal Failure in Sisters with Cystinuria and the Management of Amino Acids in Chronic Hemodialysis |
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