The pH of mitochondria of fibroblasts from a hyperornithinaemia, hyperammonaemia, homocitrullinuria‐syndrome patient

The intracellular pH of control fibroblasts and of fibroblasts of a HHH‐syndrome patient have been determined. Values of 6.94±0.15 and 7.05±0.14 for control and patient fibroblasts, respectively, were found. By means of analyses of malate in the cytosolic and particulate fractions of the fibroblasts...

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Veröffentlicht in:	Journal of inherited metabolic disease 1984-03, Vol.7 (1), p.9-11
Hauptverfasser:	Metoki, K., Hommes, F. A.
Format:	Artikel
Sprache:	eng
Schlagworte:	Acid-Base Equilibrium Ammonia - blood Citrulline - analogs & derivatives Citrulline - urine Cytosol - physiology Fibroblasts - physiology Humans Hydrogen-Ion Concentration Mitochondria - physiology Ornithine - blood Syndrome
Online-Zugang:	Volltext
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