Familial fibromuscular dysplasia of the mesenteric arteries
We have reported the case of a critically ill 17-year-old girl who had an evolving gastrointestinal infarction when she came to our institution 11 months before she died. After surgical revascularization, biopsy of the superior mesenteric artery showed FMD. We interviewed and examined all close cons...
Gespeichert in:
| Veröffentlicht in: | Southern medical journal (Birmingham, Ala.) Ala.), 1987-10, Vol.80 (10), p.1311-1316 |
|---|---|
| Hauptverfasser: | , |
| Format: | Artikel |
| Sprache: | eng |
| Schlagworte: | |
| Online-Zugang: | Volltext |
| Tags: |
Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
|
| container_end_page | 1316 |
|---|---|
| container_issue | 10 |
| container_start_page | 1311 |
| container_title | Southern medical journal (Birmingham, Ala.) |
| container_volume | 80 |
| creator | Meacham, P W Brantley, B |
| description | We have reported the case of a critically ill 17-year-old girl who had an evolving gastrointestinal infarction when she came to our institution 11 months before she died. After surgical revascularization, biopsy of the superior mesenteric artery showed FMD. We interviewed and examined all close consanguineous relatives and found abdominal bruits in the patient's younger sister and mother. Arteriograms showed total occlusion of the celiac and superior mesenteric arteries in the sister, and a subtotal celiac occlusion in the mother. Postprandial abdominal pain and constipation in the sister prompted elective mesenteric revascularization, and biopsy of the superior mesenteric artery confirmed FMD identical to that of her older sister. The mother, who is asymptomatic, has single vessel disease and has not required operative intervention. Our report strongly supports the hypothesis of a genetic basis for this arteriopathy. |
| doi_str_mv | 10.1097/00007611-198710000-00027 |
| format | Article |
| fullrecord | <record><control><sourceid>proquest_cross</sourceid><recordid>TN_cdi_proquest_miscellaneous_81047539</recordid><sourceformat>XML</sourceformat><sourcesystem>PC</sourcesystem><sourcerecordid>81047539</sourcerecordid><originalsourceid>FETCH-LOGICAL-c310t-93b529b8ee45af2698b87e877ec145eea53a87ee467a78781dc315d5a275fcad3</originalsourceid><addsrcrecordid>eNo9kEFPwzAMhXMAjTH4CUg5cSskTdKk4oQmNpAmcYFz5KauCErXkbSH_XtaVmbJerL1ni19hFDOHjgr9SMbSxecZ7w0mk9TNnauL8iSMWEyKaS5ItcpfU9GZYoFWYiiYEyaJXnaQOuDh0AbX8WuHZIbAkRaH9MhQPJAu4b2X0hbTLjvMXpHIU6K6YZcNhAS3s66Ip-bl4_1a7Z7376tn3eZE5z1WSkqlZeVQZQKmrwoTWU0Gq3RcakQQQkYFygLDdpow-sxp2oFuVaNg1qsyP3p7iF2PwOm3rY-OQwB9tgNyRrOpFaiHI3mZHSxSyliYw_RtxCPljM7sbL_rOyZlf1jNUbv5h9D1WJ9Ds6gxC-842av</addsrcrecordid><sourcetype>Aggregation Database</sourcetype><iscdi>true</iscdi><recordtype>article</recordtype><pqid>81047539</pqid></control><display><type>article</type><title>Familial fibromuscular dysplasia of the mesenteric arteries</title><source>MEDLINE</source><source>Journals@Ovid Complete</source><creator>Meacham, P W ; Brantley, B</creator><creatorcontrib>Meacham, P W ; Brantley, B</creatorcontrib><description>We have reported the case of a critically ill 17-year-old girl who had an evolving gastrointestinal infarction when she came to our institution 11 months before she died. After surgical revascularization, biopsy of the superior mesenteric artery showed FMD. We interviewed and examined all close consanguineous relatives and found abdominal bruits in the patient's younger sister and mother. Arteriograms showed total occlusion of the celiac and superior mesenteric arteries in the sister, and a subtotal celiac occlusion in the mother. Postprandial abdominal pain and constipation in the sister prompted elective mesenteric revascularization, and biopsy of the superior mesenteric artery confirmed FMD identical to that of her older sister. The mother, who is asymptomatic, has single vessel disease and has not required operative intervention. Our report strongly supports the hypothesis of a genetic basis for this arteriopathy.</description><identifier>ISSN: 0038-4348</identifier><identifier>DOI: 10.1097/00007611-198710000-00027</identifier><identifier>PMID: 3660048</identifier><language>eng</language><publisher>United States</publisher><subject>Adolescent ; Adult ; Arterial Occlusive Diseases - genetics ; Celiac Artery - diagnostic imaging ; Cerebral Arterial Diseases - diagnostic imaging ; Cerebral Arterial Diseases - genetics ; Cerebral Arterial Diseases - pathology ; Female ; Fibromuscular Dysplasia - complications ; Fibromuscular Dysplasia - diagnostic imaging ; Fibromuscular Dysplasia - genetics ; Fibromuscular Dysplasia - pathology ; Humans ; Intracranial Embolism and Thrombosis - etiology ; Male ; Mesenteric Arteries - diagnostic imaging ; Mesenteric Arteries - pathology ; Mesenteric Vascular Occlusion - diagnostic imaging ; Mesenteric Vascular Occlusion - genetics ; Mesenteric Vascular Occlusion - pathology ; Radiography</subject><ispartof>Southern medical journal (Birmingham, Ala.), 1987-10, Vol.80 (10), p.1311-1316</ispartof><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c310t-93b529b8ee45af2698b87e877ec145eea53a87ee467a78781dc315d5a275fcad3</citedby></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,780,784,27924,27925</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/3660048$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Meacham, P W</creatorcontrib><creatorcontrib>Brantley, B</creatorcontrib><title>Familial fibromuscular dysplasia of the mesenteric arteries</title><title>Southern medical journal (Birmingham, Ala.)</title><addtitle>South Med J</addtitle><description>We have reported the case of a critically ill 17-year-old girl who had an evolving gastrointestinal infarction when she came to our institution 11 months before she died. After surgical revascularization, biopsy of the superior mesenteric artery showed FMD. We interviewed and examined all close consanguineous relatives and found abdominal bruits in the patient's younger sister and mother. Arteriograms showed total occlusion of the celiac and superior mesenteric arteries in the sister, and a subtotal celiac occlusion in the mother. Postprandial abdominal pain and constipation in the sister prompted elective mesenteric revascularization, and biopsy of the superior mesenteric artery confirmed FMD identical to that of her older sister. The mother, who is asymptomatic, has single vessel disease and has not required operative intervention. Our report strongly supports the hypothesis of a genetic basis for this arteriopathy.</description><subject>Adolescent</subject><subject>Adult</subject><subject>Arterial Occlusive Diseases - genetics</subject><subject>Celiac Artery - diagnostic imaging</subject><subject>Cerebral Arterial Diseases - diagnostic imaging</subject><subject>Cerebral Arterial Diseases - genetics</subject><subject>Cerebral Arterial Diseases - pathology</subject><subject>Female</subject><subject>Fibromuscular Dysplasia - complications</subject><subject>Fibromuscular Dysplasia - diagnostic imaging</subject><subject>Fibromuscular Dysplasia - genetics</subject><subject>Fibromuscular Dysplasia - pathology</subject><subject>Humans</subject><subject>Intracranial Embolism and Thrombosis - etiology</subject><subject>Male</subject><subject>Mesenteric Arteries - diagnostic imaging</subject><subject>Mesenteric Arteries - pathology</subject><subject>Mesenteric Vascular Occlusion - diagnostic imaging</subject><subject>Mesenteric Vascular Occlusion - genetics</subject><subject>Mesenteric Vascular Occlusion - pathology</subject><subject>Radiography</subject><issn>0038-4348</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1987</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNo9kEFPwzAMhXMAjTH4CUg5cSskTdKk4oQmNpAmcYFz5KauCErXkbSH_XtaVmbJerL1ni19hFDOHjgr9SMbSxecZ7w0mk9TNnauL8iSMWEyKaS5ItcpfU9GZYoFWYiiYEyaJXnaQOuDh0AbX8WuHZIbAkRaH9MhQPJAu4b2X0hbTLjvMXpHIU6K6YZcNhAS3s66Ip-bl4_1a7Z7376tn3eZE5z1WSkqlZeVQZQKmrwoTWU0Gq3RcakQQQkYFygLDdpow-sxp2oFuVaNg1qsyP3p7iF2PwOm3rY-OQwB9tgNyRrOpFaiHI3mZHSxSyliYw_RtxCPljM7sbL_rOyZlf1jNUbv5h9D1WJ9Ds6gxC-842av</recordid><startdate>19871001</startdate><enddate>19871001</enddate><creator>Meacham, P W</creator><creator>Brantley, B</creator><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>19871001</creationdate><title>Familial fibromuscular dysplasia of the mesenteric arteries</title><author>Meacham, P W ; Brantley, B</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c310t-93b529b8ee45af2698b87e877ec145eea53a87ee467a78781dc315d5a275fcad3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1987</creationdate><topic>Adolescent</topic><topic>Adult</topic><topic>Arterial Occlusive Diseases - genetics</topic><topic>Celiac Artery - diagnostic imaging</topic><topic>Cerebral Arterial Diseases - diagnostic imaging</topic><topic>Cerebral Arterial Diseases - genetics</topic><topic>Cerebral Arterial Diseases - pathology</topic><topic>Female</topic><topic>Fibromuscular Dysplasia - complications</topic><topic>Fibromuscular Dysplasia - diagnostic imaging</topic><topic>Fibromuscular Dysplasia - genetics</topic><topic>Fibromuscular Dysplasia - pathology</topic><topic>Humans</topic><topic>Intracranial Embolism and Thrombosis - etiology</topic><topic>Male</topic><topic>Mesenteric Arteries - diagnostic imaging</topic><topic>Mesenteric Arteries - pathology</topic><topic>Mesenteric Vascular Occlusion - diagnostic imaging</topic><topic>Mesenteric Vascular Occlusion - genetics</topic><topic>Mesenteric Vascular Occlusion - pathology</topic><topic>Radiography</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Meacham, P W</creatorcontrib><creatorcontrib>Brantley, B</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Southern medical journal (Birmingham, Ala.)</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Meacham, P W</au><au>Brantley, B</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Familial fibromuscular dysplasia of the mesenteric arteries</atitle><jtitle>Southern medical journal (Birmingham, Ala.)</jtitle><addtitle>South Med J</addtitle><date>1987-10-01</date><risdate>1987</risdate><volume>80</volume><issue>10</issue><spage>1311</spage><epage>1316</epage><pages>1311-1316</pages><issn>0038-4348</issn><abstract>We have reported the case of a critically ill 17-year-old girl who had an evolving gastrointestinal infarction when she came to our institution 11 months before she died. After surgical revascularization, biopsy of the superior mesenteric artery showed FMD. We interviewed and examined all close consanguineous relatives and found abdominal bruits in the patient's younger sister and mother. Arteriograms showed total occlusion of the celiac and superior mesenteric arteries in the sister, and a subtotal celiac occlusion in the mother. Postprandial abdominal pain and constipation in the sister prompted elective mesenteric revascularization, and biopsy of the superior mesenteric artery confirmed FMD identical to that of her older sister. The mother, who is asymptomatic, has single vessel disease and has not required operative intervention. Our report strongly supports the hypothesis of a genetic basis for this arteriopathy.</abstract><cop>United States</cop><pmid>3660048</pmid><doi>10.1097/00007611-198710000-00027</doi><tpages>6</tpages></addata></record> |
| fulltext | fulltext |
| identifier | ISSN: 0038-4348 |
| ispartof | Southern medical journal (Birmingham, Ala.), 1987-10, Vol.80 (10), p.1311-1316 |
| issn | 0038-4348 |
| language | eng |
| recordid | cdi_proquest_miscellaneous_81047539 |
| source | MEDLINE; Journals@Ovid Complete |
| subjects | Adolescent Adult Arterial Occlusive Diseases - genetics Celiac Artery - diagnostic imaging Cerebral Arterial Diseases - diagnostic imaging Cerebral Arterial Diseases - genetics Cerebral Arterial Diseases - pathology Female Fibromuscular Dysplasia - complications Fibromuscular Dysplasia - diagnostic imaging Fibromuscular Dysplasia - genetics Fibromuscular Dysplasia - pathology Humans Intracranial Embolism and Thrombosis - etiology Male Mesenteric Arteries - diagnostic imaging Mesenteric Arteries - pathology Mesenteric Vascular Occlusion - diagnostic imaging Mesenteric Vascular Occlusion - genetics Mesenteric Vascular Occlusion - pathology Radiography |
| title | Familial fibromuscular dysplasia of the mesenteric arteries |
| url | https://sfx.bib-bvb.de/sfx_tum?ctx_ver=Z39.88-2004&ctx_enc=info:ofi/enc:UTF-8&ctx_tim=2025-01-07T18%3A06%3A49IST&url_ver=Z39.88-2004&url_ctx_fmt=infofi/fmt:kev:mtx:ctx&rfr_id=info:sid/primo.exlibrisgroup.com:primo3-Article-proquest_cross&rft_val_fmt=info:ofi/fmt:kev:mtx:journal&rft.genre=article&rft.atitle=Familial%20fibromuscular%20dysplasia%20of%20the%20mesenteric%20arteries&rft.jtitle=Southern%20medical%20journal%20(Birmingham,%20Ala.)&rft.au=Meacham,%20P%20W&rft.date=1987-10-01&rft.volume=80&rft.issue=10&rft.spage=1311&rft.epage=1316&rft.pages=1311-1316&rft.issn=0038-4348&rft_id=info:doi/10.1097/00007611-198710000-00027&rft_dat=%3Cproquest_cross%3E81047539%3C/proquest_cross%3E%3Curl%3E%3C/url%3E&disable_directlink=true&sfx.directlink=off&sfx.report_link=0&rft_id=info:oai/&rft_pqid=81047539&rft_id=info:pmid/3660048&rfr_iscdi=true |