Papillary stenosis and sclerosing cholangitis in an immunodeficient child
Sclerosing cholangitis, an inflammatory disease of the biliary tree that occurs infrequently in childhood, has been recognized in combination with papillary stenosis in adults with the acquired immunodeficiency syndrome. A 10-yr-old child with a familial immunodeficiency syndrome characterized by de...
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| Veröffentlicht in: | Gastroenterology (New York, N.Y. 1943) N.Y. 1943), 1989-06, Vol.96 (6), p.1600-1603 |
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| container_title | Gastroenterology (New York, N.Y. 1943) |
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| creator | Gremse, David A. Bucuvalas, John C. Bongiovanni, Gail L. |
| description | Sclerosing cholangitis, an inflammatory disease of the biliary tree that occurs infrequently in childhood, has been recognized in combination with papillary stenosis in adults with the acquired immunodeficiency syndrome. A 10-yr-old child with a familial immunodeficiency syndrome characterized by defective T-cell function and deficiencies of immunoglobulins A and G developed papillary stenosis and sclerosing cholangitis associated with cryptosporidium enteritis. The patient presented with fever, jaundice, right upper quadrant pain, and elevated serum concentrations of transaminases and alkaline phosphatase. The pain and jaundice resolved after endoscopic sphincterotomy, but the biochemical abnormalities persisted. This case demonstrates that the combination of papillary stenosis and sclerosing cholangitis can occur in children as well as adults and may be associated with immunodeficiency syndromes other than the acquired immunodeficiency syndrome. Endoscopic sphincterotomy can provide symptomatic treatment for papillary stenosis in children with this condition, although the effect of sphincterotomy on the natural history of the sclerosing cholangitis is uncertain. |
| doi_str_mv | 10.1016/0016-5085(89)90533-7 |
| format | Article |
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A 10-yr-old child with a familial immunodeficiency syndrome characterized by defective T-cell function and deficiencies of immunoglobulins A and G developed papillary stenosis and sclerosing cholangitis associated with cryptosporidium enteritis. The patient presented with fever, jaundice, right upper quadrant pain, and elevated serum concentrations of transaminases and alkaline phosphatase. The pain and jaundice resolved after endoscopic sphincterotomy, but the biochemical abnormalities persisted. This case demonstrates that the combination of papillary stenosis and sclerosing cholangitis can occur in children as well as adults and may be associated with immunodeficiency syndromes other than the acquired immunodeficiency syndrome. Endoscopic sphincterotomy can provide symptomatic treatment for papillary stenosis in children with this condition, although the effect of sphincterotomy on the natural history of the sclerosing cholangitis is uncertain.</description><identifier>ISSN: 0016-5085</identifier><identifier>EISSN: 1528-0012</identifier><identifier>DOI: 10.1016/0016-5085(89)90533-7</identifier><identifier>PMID: 2714583</identifier><identifier>CODEN: GASTAB</identifier><language>eng</language><publisher>New York, NY: Elsevier Inc</publisher><subject>AIDS/HIV ; Ampulla of Vater - surgery ; Biological and medical sciences ; Child ; Cholangitis, Sclerosing - etiology ; Common Bile Duct Diseases - etiology ; Common Bile Duct Diseases - surgery ; Constriction, Pathologic - etiology ; Constriction, Pathologic - surgery ; Humans ; Immunodeficiencies ; Immunodeficiencies. Immunoglobulinopathies ; Immunologic Deficiency Syndromes - complications ; Immunologic Deficiency Syndromes - genetics ; Immunopathology ; Male ; Medical sciences</subject><ispartof>Gastroenterology (New York, N.Y. 1943), 1989-06, Vol.96 (6), p.1600-1603</ispartof><rights>1989</rights><rights>1990 INIST-CNRS</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c386t-e0b10654fe724c4e0011421665dfb73ea230e33cf1cebc6ae71e3a782ae944d03</citedby><cites>FETCH-LOGICAL-c386t-e0b10654fe724c4e0011421665dfb73ea230e33cf1cebc6ae71e3a782ae944d03</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktohtml>$$Uhttps://dx.doi.org/10.1016/0016-5085(89)90533-7$$EHTML$$P50$$Gelsevier$$H</linktohtml><link.rule.ids>314,780,784,3550,27924,27925,45995</link.rule.ids><backlink>$$Uhttp://pascal-francis.inist.fr/vibad/index.php?action=getRecordDetail&idt=6570214$$DView record in Pascal Francis$$Hfree_for_read</backlink><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/2714583$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Gremse, David A.</creatorcontrib><creatorcontrib>Bucuvalas, John C.</creatorcontrib><creatorcontrib>Bongiovanni, Gail L.</creatorcontrib><title>Papillary stenosis and sclerosing cholangitis in an immunodeficient child</title><title>Gastroenterology (New York, N.Y. 1943)</title><addtitle>Gastroenterology</addtitle><description>Sclerosing cholangitis, an inflammatory disease of the biliary tree that occurs infrequently in childhood, has been recognized in combination with papillary stenosis in adults with the acquired immunodeficiency syndrome. A 10-yr-old child with a familial immunodeficiency syndrome characterized by defective T-cell function and deficiencies of immunoglobulins A and G developed papillary stenosis and sclerosing cholangitis associated with cryptosporidium enteritis. The patient presented with fever, jaundice, right upper quadrant pain, and elevated serum concentrations of transaminases and alkaline phosphatase. The pain and jaundice resolved after endoscopic sphincterotomy, but the biochemical abnormalities persisted. This case demonstrates that the combination of papillary stenosis and sclerosing cholangitis can occur in children as well as adults and may be associated with immunodeficiency syndromes other than the acquired immunodeficiency syndrome. Endoscopic sphincterotomy can provide symptomatic treatment for papillary stenosis in children with this condition, although the effect of sphincterotomy on the natural history of the sclerosing cholangitis is uncertain.</description><subject>AIDS/HIV</subject><subject>Ampulla of Vater - surgery</subject><subject>Biological and medical sciences</subject><subject>Child</subject><subject>Cholangitis, Sclerosing - etiology</subject><subject>Common Bile Duct Diseases - etiology</subject><subject>Common Bile Duct Diseases - surgery</subject><subject>Constriction, Pathologic - etiology</subject><subject>Constriction, Pathologic - surgery</subject><subject>Humans</subject><subject>Immunodeficiencies</subject><subject>Immunodeficiencies. Immunoglobulinopathies</subject><subject>Immunologic Deficiency Syndromes - complications</subject><subject>Immunologic Deficiency Syndromes - genetics</subject><subject>Immunopathology</subject><subject>Male</subject><subject>Medical sciences</subject><issn>0016-5085</issn><issn>1528-0012</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1989</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNp9kE1LxDAQhoMo67r6DxR6ENFDNV9t0osgix8LC3rQc0iTqUbadG1awX9v6pY9eskQ3meGmQehU4KvCSb5DY5PmmGZXcriqsAZY6nYQ3OSUZnGjO6j-Q45REchfGKMCybJDM2oIDyTbI5WL3rj6lp3P0nowbfBhUR7mwRTQxd__j0xH22t_bvrY-R8TBPXNINvLVTOOPB9JFxtj9FBpesAJ1NdoLeH-9flU7p-flwt79apYTLvU8AlwXnGKxCUGw5xRcIpyfPMVqVgoCnDwJipiIHS5BoEAaaFpBoKzi1mC3Sxnbvp2q8BQq8aFwzEGzy0Q1BCFrkgQkSQb0ETDwkdVGrTuSZeqghWo0E16lGjHiUL9WdQjW1n0_yhbMDumiZlMT-fch2MrqtOe-PCDsszgSnhEbvdYhBdfDvoVBhlGbCuA9Mr27r_9_gFeVSMuw</recordid><startdate>19890601</startdate><enddate>19890601</enddate><creator>Gremse, David A.</creator><creator>Bucuvalas, John C.</creator><creator>Bongiovanni, Gail L.</creator><general>Elsevier Inc</general><general>Elsevier</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>19890601</creationdate><title>Papillary stenosis and sclerosing cholangitis in an immunodeficient child</title><author>Gremse, David A. ; Bucuvalas, John C. ; Bongiovanni, Gail L.</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c386t-e0b10654fe724c4e0011421665dfb73ea230e33cf1cebc6ae71e3a782ae944d03</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1989</creationdate><topic>AIDS/HIV</topic><topic>Ampulla of Vater - surgery</topic><topic>Biological and medical sciences</topic><topic>Child</topic><topic>Cholangitis, Sclerosing - etiology</topic><topic>Common Bile Duct Diseases - etiology</topic><topic>Common Bile Duct Diseases - surgery</topic><topic>Constriction, Pathologic - etiology</topic><topic>Constriction, Pathologic - surgery</topic><topic>Humans</topic><topic>Immunodeficiencies</topic><topic>Immunodeficiencies. Immunoglobulinopathies</topic><topic>Immunologic Deficiency Syndromes - complications</topic><topic>Immunologic Deficiency Syndromes - genetics</topic><topic>Immunopathology</topic><topic>Male</topic><topic>Medical sciences</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Gremse, David A.</creatorcontrib><creatorcontrib>Bucuvalas, John C.</creatorcontrib><creatorcontrib>Bongiovanni, Gail L.</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Gastroenterology (New York, N.Y. 1943)</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Gremse, David A.</au><au>Bucuvalas, John C.</au><au>Bongiovanni, Gail L.</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Papillary stenosis and sclerosing cholangitis in an immunodeficient child</atitle><jtitle>Gastroenterology (New York, N.Y. 1943)</jtitle><addtitle>Gastroenterology</addtitle><date>1989-06-01</date><risdate>1989</risdate><volume>96</volume><issue>6</issue><spage>1600</spage><epage>1603</epage><pages>1600-1603</pages><issn>0016-5085</issn><eissn>1528-0012</eissn><coden>GASTAB</coden><abstract>Sclerosing cholangitis, an inflammatory disease of the biliary tree that occurs infrequently in childhood, has been recognized in combination with papillary stenosis in adults with the acquired immunodeficiency syndrome. A 10-yr-old child with a familial immunodeficiency syndrome characterized by defective T-cell function and deficiencies of immunoglobulins A and G developed papillary stenosis and sclerosing cholangitis associated with cryptosporidium enteritis. The patient presented with fever, jaundice, right upper quadrant pain, and elevated serum concentrations of transaminases and alkaline phosphatase. The pain and jaundice resolved after endoscopic sphincterotomy, but the biochemical abnormalities persisted. This case demonstrates that the combination of papillary stenosis and sclerosing cholangitis can occur in children as well as adults and may be associated with immunodeficiency syndromes other than the acquired immunodeficiency syndrome. Endoscopic sphincterotomy can provide symptomatic treatment for papillary stenosis in children with this condition, although the effect of sphincterotomy on the natural history of the sclerosing cholangitis is uncertain.</abstract><cop>New York, NY</cop><pub>Elsevier Inc</pub><pmid>2714583</pmid><doi>10.1016/0016-5085(89)90533-7</doi><tpages>4</tpages></addata></record> |
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| identifier | ISSN: 0016-5085 |
| ispartof | Gastroenterology (New York, N.Y. 1943), 1989-06, Vol.96 (6), p.1600-1603 |
| issn | 0016-5085 1528-0012 |
| language | eng |
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| source | MEDLINE; Access via ScienceDirect (Elsevier); Alma/SFX Local Collection |
| subjects | AIDS/HIV Ampulla of Vater - surgery Biological and medical sciences Child Cholangitis, Sclerosing - etiology Common Bile Duct Diseases - etiology Common Bile Duct Diseases - surgery Constriction, Pathologic - etiology Constriction, Pathologic - surgery Humans Immunodeficiencies Immunodeficiencies. Immunoglobulinopathies Immunologic Deficiency Syndromes - complications Immunologic Deficiency Syndromes - genetics Immunopathology Male Medical sciences |
| title | Papillary stenosis and sclerosing cholangitis in an immunodeficient child |
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