Congenital Cystic Adenomatoid Malformation of the Lung Associated with Bile Duct Hypoplasia
Congenital cystic adenomatoid malformation (CCAM) is a rare lesion that affects one or two lobes of the lung. Infants are either stillborn or die shortly after birth if therapy is not started immediately. The lesion itself may be solid or cystic, manifesting in an adenomatoid increase in terminal re...
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| Veröffentlicht in: | Pathology, research and practice research and practice, 1988-11, Vol.183 (6), p.771-777 |
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| container_title | Pathology, research and practice |
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| creator | Garcia, H. Heidl, G. Stöhr, G. |
| description | Congenital cystic adenomatoid malformation (CCAM) is a rare lesion that affects one or two lobes of the lung. Infants are either stillborn or die shortly after birth if therapy is not started immediately. The lesion itself may be solid or cystic, manifesting in an adenomatoid increase in terminal respiratory structures.
C1linical, pathological and radiological findings of a child prematurely born are presented. A special feature in this case was hypoplasia of intrahepatic bile ducts, an unusual association with CCAM that has not been previously reported. Pathogenesis and embryological connotations of the two lesions are discussed. The importance of prenatal diagnosis and immediate surgical therapy after birth is stressed. |
| doi_str_mv | 10.1016/S0344-0338(88)80064-5 |
| format | Article |
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C1linical, pathological and radiological findings of a child prematurely born are presented. A special feature in this case was hypoplasia of intrahepatic bile ducts, an unusual association with CCAM that has not been previously reported. Pathogenesis and embryological connotations of the two lesions are discussed. The importance of prenatal diagnosis and immediate surgical therapy after birth is stressed.</description><identifier>ISSN: 0344-0338</identifier><identifier>EISSN: 1618-0631</identifier><identifier>DOI: 10.1016/S0344-0338(88)80064-5</identifier><identifier>PMID: 3065749</identifier><language>eng</language><publisher>Germany: Elsevier GmbH</publisher><subject>Abnormalities, Multiple - diagnosis ; Abnormalities, Multiple - etiology ; Adenomatoid Malformation of the Lung ; Adult ; Bile Duct Hypoplasia ; Bile Ducts - abnormalities ; Cystic Malformation of the Lung ; Female ; Fetal Hydrops ; Humans ; Lung - abnormalities ; Pregnancy ; Prenatal Diagnosis ; Ultrasonography</subject><ispartof>Pathology, research and practice, 1988-11, Vol.183 (6), p.771-777</ispartof><rights>1988 Gustav Fischer Verlag · Stuttgart · New York</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><cites>FETCH-LOGICAL-c308t-172ea9ad5bb006f72845d0d1b3bda969efab15a99201c0422471fd34e80990cc3</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktohtml>$$Uhttps://dx.doi.org/10.1016/S0344-0338(88)80064-5$$EHTML$$P50$$Gelsevier$$H</linktohtml><link.rule.ids>314,777,781,3537,27905,27906,45976</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/3065749$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Garcia, H.</creatorcontrib><creatorcontrib>Heidl, G.</creatorcontrib><creatorcontrib>Stöhr, G.</creatorcontrib><title>Congenital Cystic Adenomatoid Malformation of the Lung Associated with Bile Duct Hypoplasia</title><title>Pathology, research and practice</title><addtitle>Pathol Res Pract</addtitle><description>Congenital cystic adenomatoid malformation (CCAM) is a rare lesion that affects one or two lobes of the lung. Infants are either stillborn or die shortly after birth if therapy is not started immediately. The lesion itself may be solid or cystic, manifesting in an adenomatoid increase in terminal respiratory structures.
C1linical, pathological and radiological findings of a child prematurely born are presented. A special feature in this case was hypoplasia of intrahepatic bile ducts, an unusual association with CCAM that has not been previously reported. Pathogenesis and embryological connotations of the two lesions are discussed. The importance of prenatal diagnosis and immediate surgical therapy after birth is stressed.</description><subject>Abnormalities, Multiple - diagnosis</subject><subject>Abnormalities, Multiple - etiology</subject><subject>Adenomatoid Malformation of the Lung</subject><subject>Adult</subject><subject>Bile Duct Hypoplasia</subject><subject>Bile Ducts - abnormalities</subject><subject>Cystic Malformation of the Lung</subject><subject>Female</subject><subject>Fetal Hydrops</subject><subject>Humans</subject><subject>Lung - abnormalities</subject><subject>Pregnancy</subject><subject>Prenatal Diagnosis</subject><subject>Ultrasonography</subject><issn>0344-0338</issn><issn>1618-0631</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1988</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqFkE1LxDAQhoMoun78BCEn0UN10qRtepJ1_VhhxYN68hDSZKqRbrM2qbL_3q67eBUGhmHed17mIeSYwTkDll88ARciAc7lqZRnEiAXSbZFRixnMoGcs20y-pPskf0QPgCgAMF2yS6HPCtEOSKvE9--YeuibuhkGaIzdGyx9XMdvbP0QTe174bB-Zb6msZ3pLO-faPjELxxOqKl3y6-0yvXIL3uTaTT5cIvGh2cPiQ7tW4CHm36AXm5vXmeTJPZ4939ZDxLDAcZE1akqEtts6oanqiLVIrMgmUVr6wu8xJrXbFMl2UKzIBIU1Gw2nKBEsoSjOEH5GR9d9H5zx5DVHMXDDaNbtH3QRUyzwdk6SDM1kLT-RA6rNWic3PdLRUDtYKqfqGqFTElh1pBVdngO94E9NUc7Z9rQ3HYX673OHz55bBTwThsDVrXoYnKevdPwg_63oal</recordid><startdate>19881101</startdate><enddate>19881101</enddate><creator>Garcia, H.</creator><creator>Heidl, G.</creator><creator>Stöhr, G.</creator><general>Elsevier GmbH</general><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>19881101</creationdate><title>Congenital Cystic Adenomatoid Malformation of the Lung Associated with Bile Duct Hypoplasia</title><author>Garcia, H. ; Heidl, G. ; Stöhr, G.</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c308t-172ea9ad5bb006f72845d0d1b3bda969efab15a99201c0422471fd34e80990cc3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1988</creationdate><topic>Abnormalities, Multiple - diagnosis</topic><topic>Abnormalities, Multiple - etiology</topic><topic>Adenomatoid Malformation of the Lung</topic><topic>Adult</topic><topic>Bile Duct Hypoplasia</topic><topic>Bile Ducts - abnormalities</topic><topic>Cystic Malformation of the Lung</topic><topic>Female</topic><topic>Fetal Hydrops</topic><topic>Humans</topic><topic>Lung - abnormalities</topic><topic>Pregnancy</topic><topic>Prenatal Diagnosis</topic><topic>Ultrasonography</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Garcia, H.</creatorcontrib><creatorcontrib>Heidl, G.</creatorcontrib><creatorcontrib>Stöhr, G.</creatorcontrib><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Pathology, research and practice</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Garcia, H.</au><au>Heidl, G.</au><au>Stöhr, G.</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Congenital Cystic Adenomatoid Malformation of the Lung Associated with Bile Duct Hypoplasia</atitle><jtitle>Pathology, research and practice</jtitle><addtitle>Pathol Res Pract</addtitle><date>1988-11-01</date><risdate>1988</risdate><volume>183</volume><issue>6</issue><spage>771</spage><epage>777</epage><pages>771-777</pages><issn>0344-0338</issn><eissn>1618-0631</eissn><abstract>Congenital cystic adenomatoid malformation (CCAM) is a rare lesion that affects one or two lobes of the lung. Infants are either stillborn or die shortly after birth if therapy is not started immediately. The lesion itself may be solid or cystic, manifesting in an adenomatoid increase in terminal respiratory structures.
C1linical, pathological and radiological findings of a child prematurely born are presented. A special feature in this case was hypoplasia of intrahepatic bile ducts, an unusual association with CCAM that has not been previously reported. Pathogenesis and embryological connotations of the two lesions are discussed. The importance of prenatal diagnosis and immediate surgical therapy after birth is stressed.</abstract><cop>Germany</cop><pub>Elsevier GmbH</pub><pmid>3065749</pmid><doi>10.1016/S0344-0338(88)80064-5</doi><tpages>7</tpages></addata></record> |
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| ispartof | Pathology, research and practice, 1988-11, Vol.183 (6), p.771-777 |
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| language | eng |
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| source | MEDLINE; Elsevier ScienceDirect Journals |
| subjects | Abnormalities, Multiple - diagnosis Abnormalities, Multiple - etiology Adenomatoid Malformation of the Lung Adult Bile Duct Hypoplasia Bile Ducts - abnormalities Cystic Malformation of the Lung Female Fetal Hydrops Humans Lung - abnormalities Pregnancy Prenatal Diagnosis Ultrasonography |
| title | Congenital Cystic Adenomatoid Malformation of the Lung Associated with Bile Duct Hypoplasia |
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