Blood exchange and transfusion therapy for acute cholestasis in protoporphyria
Acute cholestasis is a rare complication of EPP with a high mortality rate despite extensive treatment with corticosteroids, cholestyramine, and antioxidants. A single survivor, reported in the literature, was treated with blood exchange transfusions. We treated two EPP patients with blood exchange...
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| Veröffentlicht in: | Digestive diseases and sciences 1988-12, Vol.33 (12), p.1621-1625 |
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| container_issue | 12 |
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| container_title | Digestive diseases and sciences |
| container_volume | 33 |
| creator | VAN WIJK, H. J VAN HATTUM, J BAART DE LA FAILLE, H VAN DEN BERG, J. W. O EDIXHOVEN-BOSDIJK, A WILSON, J. H. P |
| description | Acute cholestasis is a rare complication of EPP with a high mortality rate despite extensive treatment with corticosteroids, cholestyramine, and antioxidants. A single survivor, reported in the literature, was treated with blood exchange transfusions. We treated two EPP patients with blood exchange and additional blood transfusions which resulted in full clinical and biochemical recovery from the cholestasis and accompanying hepatitis. Recurrences of the cholestasis and hepatitis could repeatedly be corrected by additional blood transfusions. |
| doi_str_mv | 10.1007/BF01535955 |
| format | Article |
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Recurrences of the cholestasis and hepatitis could repeatedly be corrected by additional blood transfusions.</description><identifier>ISSN: 0163-2116</identifier><identifier>EISSN: 1573-2568</identifier><identifier>DOI: 10.1007/BF01535955</identifier><identifier>PMID: 3197588</identifier><identifier>CODEN: DDSCDJ</identifier><language>eng</language><publisher>Heidelberg: Springer</publisher><subject>Acute Disease ; Adult ; Biological and medical sciences ; Blood Transfusion ; Cholestasis - etiology ; Cholestasis - therapy ; Exchange Transfusion, Whole Blood ; Female ; Humans ; Liver Diseases - complications ; Male ; Medical sciences ; Metabolic diseases ; Other metabolic disorders ; Pigments (porphyrias, hyperbilirubinemias...) ; Porphyrias - complications</subject><ispartof>Digestive diseases and sciences, 1988-12, Vol.33 (12), p.1621-1625</ispartof><rights>1989 INIST-CNRS</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c311t-4f779c0e80f7982a0730a8852a19627b859a937aea6a4b06b41bab050c4bd5213</citedby><cites>FETCH-LOGICAL-c311t-4f779c0e80f7982a0730a8852a19627b859a937aea6a4b06b41bab050c4bd5213</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><link.rule.ids>314,780,784,27924,27925</link.rule.ids><backlink>$$Uhttp://pascal-francis.inist.fr/vibad/index.php?action=getRecordDetail&idt=7137141$$DView record in Pascal Francis$$Hfree_for_read</backlink><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/3197588$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>VAN WIJK, H. 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Recurrences of the cholestasis and hepatitis could repeatedly be corrected by additional blood transfusions.</description><subject>Acute Disease</subject><subject>Adult</subject><subject>Biological and medical sciences</subject><subject>Blood Transfusion</subject><subject>Cholestasis - etiology</subject><subject>Cholestasis - therapy</subject><subject>Exchange Transfusion, Whole Blood</subject><subject>Female</subject><subject>Humans</subject><subject>Liver Diseases - complications</subject><subject>Male</subject><subject>Medical sciences</subject><subject>Metabolic diseases</subject><subject>Other metabolic disorders</subject><subject>Pigments (porphyrias, hyperbilirubinemias...)</subject><subject>Porphyrias - complications</subject><issn>0163-2116</issn><issn>1573-2568</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1988</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNpFkEFLxDAQRoMo67p68S7kIB6EaqZpmuToLq4Ki170XKZpaivdpiYtuP_eypb1NAPf45vhEXIJ7A4Yk_fLNQPBhRbiiMxBSB7FIlXHZM4gHXeA9JSchfDFGNMS0hmZcdBSKDUnr8vGuYLaH1Nh-2kptgXtPbahHELtWtpX1mO3o6XzFM3QW2oq19jQY6gDrVvaede7zvmu2vkaz8lJiU2wF9NckI_14_vqOdq8Pb2sHjaR4QB9lJRSasOsYqXUKkYmOUOlRIyg01jmSmjUXKLFFJOcpXkCOeZMMJPkhYiBL8jNvnc8_z2M72TbOhjbNNhaN4RMKpEKEHoEb_eg8S4Eb8us8_UW_S4Dlv3Jy_7ljfDV1DrkW1sc0MnWmF9POQaDTTl6MnU4YBK4hAT4LxXVdgI</recordid><startdate>19881201</startdate><enddate>19881201</enddate><creator>VAN WIJK, H. 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P</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Blood exchange and transfusion therapy for acute cholestasis in protoporphyria</atitle><jtitle>Digestive diseases and sciences</jtitle><addtitle>Dig Dis Sci</addtitle><date>1988-12-01</date><risdate>1988</risdate><volume>33</volume><issue>12</issue><spage>1621</spage><epage>1625</epage><pages>1621-1625</pages><issn>0163-2116</issn><eissn>1573-2568</eissn><coden>DDSCDJ</coden><abstract>Acute cholestasis is a rare complication of EPP with a high mortality rate despite extensive treatment with corticosteroids, cholestyramine, and antioxidants. A single survivor, reported in the literature, was treated with blood exchange transfusions. We treated two EPP patients with blood exchange and additional blood transfusions which resulted in full clinical and biochemical recovery from the cholestasis and accompanying hepatitis. 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| fulltext | fulltext |
| identifier | ISSN: 0163-2116 |
| ispartof | Digestive diseases and sciences, 1988-12, Vol.33 (12), p.1621-1625 |
| issn | 0163-2116 1573-2568 |
| language | eng |
| recordid | cdi_proquest_miscellaneous_78565159 |
| source | MEDLINE; SpringerNature Journals |
| subjects | Acute Disease Adult Biological and medical sciences Blood Transfusion Cholestasis - etiology Cholestasis - therapy Exchange Transfusion, Whole Blood Female Humans Liver Diseases - complications Male Medical sciences Metabolic diseases Other metabolic disorders Pigments (porphyrias, hyperbilirubinemias...) Porphyrias - complications |
| title | Blood exchange and transfusion therapy for acute cholestasis in protoporphyria |
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