Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report
Summary Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifaetorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasial who has a documented family histor...
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| Veröffentlicht in: | British journal of dermatology (1951) 1996-06, Vol.134 (6), p.1144-1146 |
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| container_issue | 6 |
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| container_title | British journal of dermatology (1951) |
| container_volume | 134 |
| creator | FITZGERALD, E.A. CONNELLY, C.S. PURCELL, S.M. KANTOR, G.R. |
| description | Summary
Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifaetorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasial who has a documented family history of two sisters with lichen sclerosus et atrophicus. She presented with vulvar pruritas in association with dyspareunia. and biopsy of atrophic white vulvar lesions was consistent with lichen sclerosus et atrophicus. Lichen sclerosus et atrophicus has been previously noted to occur in association with morphoea and lichen planus, although it has never been reported in conjunction with CREST syndrome. |
| doi_str_mv | 10.1046/j.1365-2133.1996.d01-921.x |
| format | Article |
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Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifaetorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasial who has a documented family history of two sisters with lichen sclerosus et atrophicus. She presented with vulvar pruritas in association with dyspareunia. and biopsy of atrophic white vulvar lesions was consistent with lichen sclerosus et atrophicus. Lichen sclerosus et atrophicus has been previously noted to occur in association with morphoea and lichen planus, although it has never been reported in conjunction with CREST syndrome.</description><identifier>ISSN: 0007-0963</identifier><identifier>EISSN: 1365-2133</identifier><identifier>DOI: 10.1046/j.1365-2133.1996.d01-921.x</identifier><identifier>PMID: 8763444</identifier><identifier>CODEN: BJDEAZ</identifier><language>eng</language><publisher>Oxford, UK: Blackwell Publishing Ltd</publisher><subject>Adult ; Biological and medical sciences ; CREST Syndrome - complications ; CREST Syndrome - pathology ; Dermatology ; Female ; Humans ; Lichen Sclerosus et Atrophicus - complications ; Lichen Sclerosus et Atrophicus - genetics ; Lichen Sclerosus et Atrophicus - pathology ; Medical sciences ; Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis ; Skin involvement in other diseases. Miscellaneous. General aspects ; Vulvar Diseases - complications ; Vulvar Diseases - pathology</subject><ispartof>British journal of dermatology (1951), 1996-06, Vol.134 (6), p.1144-1146</ispartof><rights>1996 INIST-CNRS</rights><lds50>peer_reviewed</lds50><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c3314-3e17af603abcc41460bb4bc60a1f1605790744ebb1255eb864aec9d2aaeb05483</citedby><cites>FETCH-LOGICAL-c3314-3e17af603abcc41460bb4bc60a1f1605790744ebb1255eb864aec9d2aaeb05483</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktopdf>$$Uhttps://onlinelibrary.wiley.com/doi/pdf/10.1046%2Fj.1365-2133.1996.d01-921.x$$EPDF$$P50$$Gwiley$$H</linktopdf><linktohtml>$$Uhttps://onlinelibrary.wiley.com/doi/full/10.1046%2Fj.1365-2133.1996.d01-921.x$$EHTML$$P50$$Gwiley$$H</linktohtml><link.rule.ids>314,776,780,1411,27903,27904,45553,45554</link.rule.ids><backlink>$$Uhttp://pascal-francis.inist.fr/vibad/index.php?action=getRecordDetail&idt=3102604$$DView record in Pascal Francis$$Hfree_for_read</backlink><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/8763444$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>FITZGERALD, E.A.</creatorcontrib><creatorcontrib>CONNELLY, C.S.</creatorcontrib><creatorcontrib>PURCELL, S.M.</creatorcontrib><creatorcontrib>KANTOR, G.R.</creatorcontrib><title>Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report</title><title>British journal of dermatology (1951)</title><addtitle>Br J Dermatol</addtitle><description>Summary
Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifaetorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasial who has a documented family history of two sisters with lichen sclerosus et atrophicus. She presented with vulvar pruritas in association with dyspareunia. and biopsy of atrophic white vulvar lesions was consistent with lichen sclerosus et atrophicus. Lichen sclerosus et atrophicus has been previously noted to occur in association with morphoea and lichen planus, although it has never been reported in conjunction with CREST syndrome.</description><subject>Adult</subject><subject>Biological and medical sciences</subject><subject>CREST Syndrome - complications</subject><subject>CREST Syndrome - pathology</subject><subject>Dermatology</subject><subject>Female</subject><subject>Humans</subject><subject>Lichen Sclerosus et Atrophicus - complications</subject><subject>Lichen Sclerosus et Atrophicus - genetics</subject><subject>Lichen Sclerosus et Atrophicus - pathology</subject><subject>Medical sciences</subject><subject>Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis</subject><subject>Skin involvement in other diseases. Miscellaneous. General aspects</subject><subject>Vulvar Diseases - complications</subject><subject>Vulvar Diseases - pathology</subject><issn>0007-0963</issn><issn>1365-2133</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1996</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqVkE1v1DAQhi0EKkvhJyBZCHFLmIkdJ-kFwdKWVpWQ2nLgZI29jtYrJ1nsrNr99020q71zGlnvMx9-GPuEkCNI9XWTo1BlVqAQOTaNyleAWVNg_vyKLU7Ra7YAgCqDRom37F1KGwAUUMIZO6srJaSUC_b3ijofPAUevF27nicbXBzSLnE3chrjsF17O718zymlwXoa_dDzJz-u-fL-8uGRp32_ikPnLjhxS8nx6LZDHN-zNy2F5D4c6zn7c3X5uPyV3f2-vll-v8usECgz4bCiVoEgY61EqcAYaawCwhYVlFUDlZTOGCzK0plaSXK2WRVEzkApa3HOvhzmbuPwb-fSqDufrAuBejfskq5qLKu6lBN4cQDt9L8UXau30XcU9xpBz171Rs_y9CxPz1715FVPXvXz1PzxuGVnOrc6tR5FTvnnY07JUmgj9danEyYQCgUz9u2APfng9v9xgP5x-xNxWvQCV3CUtg</recordid><startdate>199606</startdate><enddate>199606</enddate><creator>FITZGERALD, E.A.</creator><creator>CONNELLY, C.S.</creator><creator>PURCELL, S.M.</creator><creator>KANTOR, G.R.</creator><general>Blackwell Publishing Ltd</general><general>Blackwell</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>199606</creationdate><title>Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report</title><author>FITZGERALD, E.A. ; CONNELLY, C.S. ; PURCELL, S.M. ; KANTOR, G.R.</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c3314-3e17af603abcc41460bb4bc60a1f1605790744ebb1255eb864aec9d2aaeb05483</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1996</creationdate><topic>Adult</topic><topic>Biological and medical sciences</topic><topic>CREST Syndrome - complications</topic><topic>CREST Syndrome - pathology</topic><topic>Dermatology</topic><topic>Female</topic><topic>Humans</topic><topic>Lichen Sclerosus et Atrophicus - complications</topic><topic>Lichen Sclerosus et Atrophicus - genetics</topic><topic>Lichen Sclerosus et Atrophicus - pathology</topic><topic>Medical sciences</topic><topic>Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis</topic><topic>Skin involvement in other diseases. Miscellaneous. General aspects</topic><topic>Vulvar Diseases - complications</topic><topic>Vulvar Diseases - pathology</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>FITZGERALD, E.A.</creatorcontrib><creatorcontrib>CONNELLY, C.S.</creatorcontrib><creatorcontrib>PURCELL, S.M.</creatorcontrib><creatorcontrib>KANTOR, G.R.</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>British journal of dermatology (1951)</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>FITZGERALD, E.A.</au><au>CONNELLY, C.S.</au><au>PURCELL, S.M.</au><au>KANTOR, G.R.</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report</atitle><jtitle>British journal of dermatology (1951)</jtitle><addtitle>Br J Dermatol</addtitle><date>1996-06</date><risdate>1996</risdate><volume>134</volume><issue>6</issue><spage>1144</spage><epage>1146</epage><pages>1144-1146</pages><issn>0007-0963</issn><eissn>1365-2133</eissn><coden>BJDEAZ</coden><abstract>Summary
Lichen sclerosus et atrophicus is an uncommon disease which appears to be multifaetorial in aetiology. We describe a case of a young woman with CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal dysfunction, sclerodactyly and telangiectasial who has a documented family history of two sisters with lichen sclerosus et atrophicus. She presented with vulvar pruritas in association with dyspareunia. and biopsy of atrophic white vulvar lesions was consistent with lichen sclerosus et atrophicus. Lichen sclerosus et atrophicus has been previously noted to occur in association with morphoea and lichen planus, although it has never been reported in conjunction with CREST syndrome.</abstract><cop>Oxford, UK</cop><pub>Blackwell Publishing Ltd</pub><pmid>8763444</pmid><doi>10.1046/j.1365-2133.1996.d01-921.x</doi><tpages>3</tpages></addata></record> |
| fulltext | fulltext |
| identifier | ISSN: 0007-0963 |
| ispartof | British journal of dermatology (1951), 1996-06, Vol.134 (6), p.1144-1146 |
| issn | 0007-0963 1365-2133 |
| language | eng |
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| source | MEDLINE; Wiley Online Library Journals Frontfile Complete; Oxford University Press Journals All Titles (1996-Current) |
| subjects | Adult Biological and medical sciences CREST Syndrome - complications CREST Syndrome - pathology Dermatology Female Humans Lichen Sclerosus et Atrophicus - complications Lichen Sclerosus et Atrophicus - genetics Lichen Sclerosus et Atrophicus - pathology Medical sciences Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis Skin involvement in other diseases. Miscellaneous. General aspects Vulvar Diseases - complications Vulvar Diseases - pathology |
| title | Familial lichen sclerosus et atrophicus in association with CREST syndrome: a case report |
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