Morphological observations in skeletal muscle from patients with a mitochondrial myopathy

Mitochondrial metabolic dysfunction is considered to be the cause of certain congenital myopathies and a number of multisystem disorders in humans. The morphological hallmark of these diseases is the ‘ragged red’ fibre, which shows abnormally intensive oxidative enzyme reactions. Electron microscopy...

Ausführliche Beschreibung

Bibliographische Detailangaben

Veröffentlicht in:	Journal of inherited metabolic disease 1987-03, Vol.10 (S1), p.62-80
Hauptverfasser:	Stadhouders, A. M., Sengers, R. C. A.
Format:	Artikel
Sprache:	eng
Schlagworte:	Crystallization Humans Intracellular Membranes - pathology Lipid Peroxides - metabolism Microscopy, Electron Mitochondria, Muscle - pathology Muscular Diseases - congenital Muscular Diseases - pathology Proteins - metabolism
Online-Zugang:	Volltext
Tags:	Tag hinzufügen Keine Tags, Fügen Sie den ersten Tag hinzu!