Metabolism of sphingomyelin in cultured skin fibroblasts from patients with different types of Niemann-Pick disease

The metabolism of [choline-methyl-14C]sphingomyelin in cultured skin fibroblasts from patients with different types of Niemann-Pick disease was measured 1 and 3 days after uptake from the media. The cell lines obtained from type A disease had more than 95% unhydrolyzed sphingomyelin in situ on day 3...

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Veröffentlicht in:	Tohoku journal of experimental medicine 1986-04, Vol.148 (4), p.365-371
Hauptverfasser:	Nakashima, M, Kudoh, T, Sukegawa, K, Maruyama, K, Orii, T
Format:	Artikel
Sprache:	eng
Schlagworte:	Cells, Cultured Fibroblasts - enzymology Fibroblasts - metabolism Hexosaminidases - metabolism Humans Niemann-Pick Diseases - enzymology Niemann-Pick Diseases - metabolism Skin - enzymology Skin - metabolism Sphingomyelin Phosphodiesterase - metabolism Sphingomyelins - metabolism
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