Hirschsprung's disease in young adults

Hirschsprung's disease is rarely seen in the young adult, and presents unique problems in management because of the massive dilatation and hypertrophy that occur proximal to the aganglionic rectum or the rectosigmoid colon. The diagnosis, which may be suspected by barium enema, is confirmed by...

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Veröffentlicht in:The American journal of surgery 1986, Vol.151 (1), p.104-109
Hauptverfasser: Starling, James R., Croom, Robert D., Thomas, Colin G.
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container_title The American journal of surgery
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creator Starling, James R.
Croom, Robert D.
Thomas, Colin G.
description Hirschsprung's disease is rarely seen in the young adult, and presents unique problems in management because of the massive dilatation and hypertrophy that occur proximal to the aganglionic rectum or the rectosigmoid colon. The diagnosis, which may be suspected by barium enema, is confirmed by suction or full-thickness biopsy of the rectum that may be complemented by anal manometry. Based on our experience with eight patients, a two-stage surgical reconstruction is recommended, with a preliminary sigmoid colostomy through the normally innervated colon and an associated defunctionalized stoma constituting the initial operation. The distal colonic stoma permits cleansing of the caudal colon while the normally innervated proximal colon reverts to near normal caliber, usually within 2 to 6 months. This approach is in accord with the recommendation of Fairgrieve [2]. Reconstruction using a Duhamel or Soave procedure has given good results. The Duhamel procedure seems preferable when a considerable discrepancy remains between the ganglionic and aganglionic segments of rectum [4].
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Liver. Pancreas. Abdomen</topic><topic>Hirschsprung Disease - diagnosis</topic><topic>Hirschsprung Disease - surgery</topic><topic>Humans</topic><topic>Intestinal Obstruction - diagnosis</topic><topic>Male</topic><topic>Malformations</topic><topic>Manometry</topic><topic>Medical sciences</topic><topic>Methods</topic><topic>Rectum - innervation</topic><topic>Rectum - surgery</topic><topic>Reoperation</topic><topic>Stomach. Duodenum. Small intestine. Colon. Rectum. 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subjects Adolescent
Adult
Biological and medical sciences
Colostomy
Constipation - diagnosis
Diagnosis, Differential
Follow-Up Studies
Gastroenterology. Liver. Pancreas. Abdomen
Hirschsprung Disease - diagnosis
Hirschsprung Disease - surgery
Humans
Intestinal Obstruction - diagnosis
Male
Malformations
Manometry
Medical sciences
Methods
Rectum - innervation
Rectum - surgery
Reoperation
Stomach. Duodenum. Small intestine. Colon. Rectum. Anus
title Hirschsprung's disease in young adults
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