A bioassay for determining biotinidase activity and for discriminating biocytin from biotin using holocarboxylase synthetase‐deficient cultured fibroblasts

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Veröffentlicht in:Journal of inherited metabolic disease 1985-06, Vol.8 (S2), p.101-102
Hauptverfasser: Weiner, D. L., Grier, R. E., Wolf, B.
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container_end_page 102
container_issue S2
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container_title Journal of inherited metabolic disease
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creator Weiner, D. L.
Grier, R. E.
Wolf, B.
description
doi_str_mv 10.1007/BF01811478
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1573-2665
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source MEDLINE; SpringerLink Journals
subjects Amidohydrolases - analysis
Amidohydrolases - deficiency
Aminoacid disorders
Biological and medical sciences
Biological Assay
Biotin - metabolism
Biotinidase
Carbon-Nitrogen Ligases
Carboxy-Lyases - analysis
Cells, Cultured
Errors of metabolism
Fibroblasts - enzymology
Humans
Ligases - deficiency
Lysine - analogs & derivatives
Lysine - metabolism
Medical sciences
Metabolic diseases
Methylmalonyl-CoA Decarboxylase
title A bioassay for determining biotinidase activity and for discriminating biocytin from biotin using holocarboxylase synthetase‐deficient cultured fibroblasts
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