Compressive myelopathy in maroteaux-lamy syndrome: Clinical and pathological findings

Compressive myelopathy in maroteaux-lamy syndrome: Clinical and pathological findings

A 41‐year‐old woman with Maroteaux‐Lamy syndrome developed spastic tetraparesis due to a compressive cervical myelopathy. There was substantial improvement following lammectomy and excision of the markedly thickened dura. Light and electron microscopic studies showed extensive accumulations of ballo...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Veröffentlicht in:Annals of neurology 1980-09, Vol.8 (3), p.336-340
Hauptverfasser: Young, Richard, Kleinman, George, Ojemann, Robert G., Kolodny, Edwin, Davis, Kenneth, Halperin, John, Zalneraitis, Edwin, Robert DeLong, G.
Format: Artikel
Sprache:eng
Schlagworte:
Adult
Dura Mater - pathology
Female
Humans
Mucopolysaccharidoses - complications
Mucopolysaccharidosis VI - complications
Mucopolysaccharidosis VI - pathology
Muscle Spasticity - etiology
Neck
Quadriplegia - etiology
Spinal Cord Compression - etiology
Online-Zugang:Volltext
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!
Beschreibung
Zusammenfassung:A 41‐year‐old woman with Maroteaux‐Lamy syndrome developed spastic tetraparesis due to a compressive cervical myelopathy. There was substantial improvement following lammectomy and excision of the markedly thickened dura. Light and electron microscopic studies showed extensive accumulations of balloon cells in the dura.
ISSN:0364-5134
1531-8249
DOI:10.1002/ana.410080321