Treatment Dilemma: Conservative versus Surgery in Cutis Aplasia Congenita

Abstract Cutis aplasia congenita (CAC), a congenital absence of skin and its appendages, may extend into underlying muscles and bones. The scalp is the commonest site and it may be associated with acrania. CAC presents either as a thin transparent membrane, a black eschar, an ulcer or a healed scar....

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Veröffentlicht in:European journal of pediatric surgery 2003-04, Vol.13 (2), p.125-129
Hauptverfasser: Bang, R. L., Ghoneim, I. E., Gang, R. K., Al Najjadah, I.
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container_issue 2
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container_title European journal of pediatric surgery
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creator Bang, R. L.
Ghoneim, I. E.
Gang, R. K.
Al Najjadah, I.
description Abstract Cutis aplasia congenita (CAC), a congenital absence of skin and its appendages, may extend into underlying muscles and bones. The scalp is the commonest site and it may be associated with acrania. CAC presents either as a thin transparent membrane, a black eschar, an ulcer or a healed scar. The dilemma of either immediate surgical management or conservative treatment is much more pronounced in the presence of acrania. Two patients with scalp lesions measuring 12 × 8 cm and 14 × 12 cm respectively and one patient with 4 cm wide circumferential trunk cutis aplasia treated conservatively are presented. The conservative treatment is simple, easy to carry out, and effective even for large defects; therefore, it is recommended in cutis aplasia congenita till complete healing. Surgical interventions such as tissue expansion and resurfacing, contracture release, etc. are for the correction of subsequent deformity at a later date.
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The conservative treatment is simple, easy to carry out, and effective even for large defects; therefore, it is recommended in cutis aplasia congenita till complete healing. Surgical interventions such as tissue expansion and resurfacing, contracture release, etc. are for the correction of subsequent deformity at a later date.</description><subject>Biological and medical sciences</subject><subject>Case Report</subject><subject>Dermatology</subject><subject>Female</subject><subject>Health participants</subject><subject>Hereditary diseases of the skin. Congenital diseases of the skin. Haemangioma of the skin, of mucosae and of soft tissue</subject><subject>Humans</subject><subject>Infant, Newborn</subject><subject>Male</subject><subject>Medical sciences</subject><subject>Public health. Hygiene</subject><subject>Public health. Hygiene-occupational medicine</subject><subject>Skin Abnormalities - surgery</subject><subject>Skin Abnormalities - therapy</subject><subject>Skull - abnormalities</subject><subject>Tissue Expansion</subject><issn>0939-7248</issn><issn>1439-359X</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2003</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNpt0D1PwzAQgGELgaAUNmaUBRYInO04jtmq8ikhMQASm-WkF3CVj-JLKvXfk9JKLEx3w6M76WXshMMVB6WuKRYAMpZGpWKHjXgiTSyV-dhlIzDDrkWSHbBDojkAT4yAfXbAhdapSNIRe3oL6Loamy669RXWtbuJpm1DGJau80uMlhiop-i1D58YVpFvomnfeYomi8qRd2v8iY3v3BHbK11FeLydY_Z-f_c2fYyfXx6eppPnuJBKdvGsFNxwlwJqzYXSGvPcZLx0Ktc5l5DNFIBWgBxknjqdprlRTnEjhZQoMjlm55u7i9B-90idrT0VWFWuwbYnq6UURoMY4OUGFqElCljaRfC1CyvLwa7TWbLrdPY33cBPt3f7vMbZH962GsDZFjgqXFUG1xSe_lySKUgSM7iLjeu-PNZo520fmqHI_29_AJPJglY</recordid><startdate>20030401</startdate><enddate>20030401</enddate><creator>Bang, R. L.</creator><creator>Ghoneim, I. E.</creator><creator>Gang, R. 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Haemangioma of the skin, of mucosae and of soft tissue</topic><topic>Humans</topic><topic>Infant, Newborn</topic><topic>Male</topic><topic>Medical sciences</topic><topic>Public health. Hygiene</topic><topic>Public health. Hygiene-occupational medicine</topic><topic>Skin Abnormalities - surgery</topic><topic>Skin Abnormalities - therapy</topic><topic>Skull - abnormalities</topic><topic>Tissue Expansion</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Bang, R. L.</creatorcontrib><creatorcontrib>Ghoneim, I. E.</creatorcontrib><creatorcontrib>Gang, R. 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subjects Biological and medical sciences
Case Report
Dermatology
Female
Health participants
Hereditary diseases of the skin. Congenital diseases of the skin. Haemangioma of the skin, of mucosae and of soft tissue
Humans
Infant, Newborn
Male
Medical sciences
Public health. Hygiene
Public health. Hygiene-occupational medicine
Skin Abnormalities - surgery
Skin Abnormalities - therapy
Skull - abnormalities
Tissue Expansion
title Treatment Dilemma: Conservative versus Surgery in Cutis Aplasia Congenita
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