Adult Hirschsprung's disease

Two cases of adult Hirschsprung's disease are reported along with a review of 47 cases reported in the literature. Chronic constipation is present in almost all cases. The barium enema examination may suggest the diagnosis if an area of smooth narrowing with proximal dilatation is seen (83%), b...

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Veröffentlicht in:	Clinical radiology 1991-10, Vol.44 (4), p.257-259
Hauptverfasser:	Crocker, N.L., Messmer, J.M.
Format:	Artikel
Sprache:	eng
Schlagworte:	Adult Biological and medical sciences Colon - diagnostic imaging Constipation - etiology Hirschsprung Disease - complications Hirschsprung Disease - diagnostic imaging Hirschsprung Disease - physiopathology Humans Investigative techniques, diagnostic techniques (general aspects) Male Medical sciences Radiodiagnosis. Nmr imagery. Nmr spectrometry Radiography Rectum - diagnostic imaging Rectum - innervation Rectum - physiopathology
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container_title	Clinical radiology
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creator	Crocker, N.L. Messmer, J.M.
description	Two cases of adult Hirschsprung's disease are reported along with a review of 47 cases reported in the literature. Chronic constipation is present in almost all cases. The barium enema examination may suggest the diagnosis if an area of smooth narrowing with proximal dilatation is seen (83%), but biopsy proof of absence of ganglion cells is necessary. Fourteen per cent of patients had a dilatated colon without a narrowed segment. Anal manometry is helpful if it demonstrates absence of normal anorectal inhibitory reflex. Total colonic aganglionosis in the adult has been reported, but is exceptionally unusual. The diagnosis of adult Hirschsprung's disease should be suspected in patients with a history of chronic constipation and appropriate radiographic findings.
doi_str_mv	10.1016/S0009-9260(05)80191-6
format	Article
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Chronic constipation is present in almost all cases. The barium enema examination may suggest the diagnosis if an area of smooth narrowing with proximal dilatation is seen (83%), but biopsy proof of absence of ganglion cells is necessary. Fourteen per cent of patients had a dilatated colon without a narrowed segment. Anal manometry is helpful if it demonstrates absence of normal anorectal inhibitory reflex. Total colonic aganglionosis in the adult has been reported, but is exceptionally unusual. The diagnosis of adult Hirschsprung's disease should be suspected in patients with a history of chronic constipation and appropriate radiographic findings.</description><identifier>ISSN: 0009-9260</identifier><identifier>EISSN: 1365-229X</identifier><identifier>DOI: 10.1016/S0009-9260(05)80191-6</identifier><identifier>PMID: 1959304</identifier><identifier>CODEN: CLRAAG</identifier><language>eng</language><publisher>Amsterdam: Elsevier Ltd</publisher><subject>Adult ; Biological and medical sciences ; Colon - diagnostic imaging ; Constipation - etiology ; Hirschsprung Disease - complications ; Hirschsprung Disease - diagnostic imaging ; Hirschsprung Disease - physiopathology ; Humans ; Investigative techniques, diagnostic techniques (general aspects) ; Male ; Medical sciences ; Radiodiagnosis. Nmr imagery. 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Chronic constipation is present in almost all cases. The barium enema examination may suggest the diagnosis if an area of smooth narrowing with proximal dilatation is seen (83%), but biopsy proof of absence of ganglion cells is necessary. Fourteen per cent of patients had a dilatated colon without a narrowed segment. Anal manometry is helpful if it demonstrates absence of normal anorectal inhibitory reflex. Total colonic aganglionosis in the adult has been reported, but is exceptionally unusual. The diagnosis of adult Hirschsprung's disease should be suspected in patients with a history of chronic constipation and appropriate radiographic findings.</description><subject>Adult</subject><subject>Biological and medical sciences</subject><subject>Colon - diagnostic imaging</subject><subject>Constipation - etiology</subject><subject>Hirschsprung Disease - complications</subject><subject>Hirschsprung Disease - diagnostic imaging</subject><subject>Hirschsprung Disease - physiopathology</subject><subject>Humans</subject><subject>Investigative techniques, diagnostic techniques (general aspects)</subject><subject>Male</subject><subject>Medical sciences</subject><subject>Radiodiagnosis. Nmr imagery. Nmr spectrometry</subject><subject>Radiography</subject><subject>Rectum - diagnostic imaging</subject><subject>Rectum - innervation</subject><subject>Rectum - physiopathology</subject><issn>0009-9260</issn><issn>1365-229X</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>1991</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqFkD1PwzAQhi0EKqXwD6jUAfExBOw4tuMJVRVQpEoMdGCzHOcCRmlafAkS_56kqcrIdDrd43vPDyFjRm8ZZfLulVKqIx1Lek3FTUqZZpE8IEPGpYjiWL8dkuEeOSYniJ9dm8TJgAyYFprTZEjOp3lT1pO5D-g-cBOa6v0KJ7lHsAin5KiwJcLZro7I8vFhOZtHi5en59l0Ebl2Rx0BuFRlIBhVPJWZllLmMhYKJHcZdWlmHVc60ZngRWaZlZznWoFIIIUilnxELvu1m7D-agBrs_LooCxtBesGjYoFVVSyFhQ96MIaMUBhNsGvbPgxjJpOitlKMd2PDRVmK8V0AeNdQJOtIP971Vto5xe7uUVnyyLYynncY6KNl0y12H2PQevi20Mw6DxUDnIfwNUmX_t_DvkF47179Q</recordid><startdate>199110</startdate><enddate>199110</enddate><creator>Crocker, N.L.</creator><creator>Messmer, J.M.</creator><general>Elsevier Ltd</general><general>Elsevier</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>199110</creationdate><title>Adult Hirschsprung's disease</title><author>Crocker, N.L. ; Messmer, J.M.</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c304t-eec87be5107386b9666d6257e63cb0c8bac37949b53fba1a633d97e54e8ef263</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>1991</creationdate><topic>Adult</topic><topic>Biological and medical sciences</topic><topic>Colon - diagnostic imaging</topic><topic>Constipation - etiology</topic><topic>Hirschsprung Disease - complications</topic><topic>Hirschsprung Disease - diagnostic imaging</topic><topic>Hirschsprung Disease - physiopathology</topic><topic>Humans</topic><topic>Investigative techniques, diagnostic techniques (general aspects)</topic><topic>Male</topic><topic>Medical sciences</topic><topic>Radiodiagnosis. Nmr imagery. Nmr spectrometry</topic><topic>Radiography</topic><topic>Rectum - diagnostic imaging</topic><topic>Rectum - innervation</topic><topic>Rectum - physiopathology</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Crocker, N.L.</creatorcontrib><creatorcontrib>Messmer, J.M.</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Clinical radiology</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Crocker, N.L.</au><au>Messmer, J.M.</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Adult Hirschsprung's disease</atitle><jtitle>Clinical radiology</jtitle><addtitle>Clin Radiol</addtitle><date>1991-10</date><risdate>1991</risdate><volume>44</volume><issue>4</issue><spage>257</spage><epage>259</epage><pages>257-259</pages><issn>0009-9260</issn><eissn>1365-229X</eissn><coden>CLRAAG</coden><abstract>Two cases of adult Hirschsprung's disease are reported along with a review of 47 cases reported in the literature. Chronic constipation is present in almost all cases. The barium enema examination may suggest the diagnosis if an area of smooth narrowing with proximal dilatation is seen (83%), but biopsy proof of absence of ganglion cells is necessary. Fourteen per cent of patients had a dilatated colon without a narrowed segment. Anal manometry is helpful if it demonstrates absence of normal anorectal inhibitory reflex. Total colonic aganglionosis in the adult has been reported, but is exceptionally unusual. The diagnosis of adult Hirschsprung's disease should be suspected in patients with a history of chronic constipation and appropriate radiographic findings.</abstract><cop>Amsterdam</cop><pub>Elsevier Ltd</pub><pmid>1959304</pmid><doi>10.1016/S0009-9260(05)80191-6</doi><tpages>3</tpages></addata></record>
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source	MEDLINE; Elsevier ScienceDirect Journals Complete
subjects	Adult Biological and medical sciences Colon - diagnostic imaging Constipation - etiology Hirschsprung Disease - complications Hirschsprung Disease - diagnostic imaging Hirschsprung Disease - physiopathology Humans Investigative techniques, diagnostic techniques (general aspects) Male Medical sciences Radiodiagnosis. Nmr imagery. Nmr spectrometry Radiography Rectum - diagnostic imaging Rectum - innervation Rectum - physiopathology
title	Adult Hirschsprung's disease
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