Prolonged survival with hydranencephaly: report of two patients and literature review
Infants with hydranencephaly are presumed to have a reduced life expectancy, with a survival of several weeks to months. Rarely, patients with prolonged survival have been reported, but these infants may have had other neurologic conditions that mimicked hydranencephaly, such as massive hydrocephalu...
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| Veröffentlicht in: | Pediatric neurology 2000-07, Vol.23 (1), p.80-84 |
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| container_title | Pediatric neurology |
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| creator | McAbee, Gary N Chan, Allison Erde, Edmund L |
| description | Infants with hydranencephaly are presumed to have a reduced life expectancy, with a survival of several weeks to months. Rarely, patients with prolonged survival have been reported, but these infants may have had other neurologic conditions that mimicked hydranencephaly, such as massive hydrocephalus or holoprosencephaly. We report two infants with prenatally acquired hydranencephaly who survived for 66 and 24 months. We reviewed published reports to ascertain the clinical and laboratory features associated with survival of more than 6 months. This review demonstrates that prolonged survival up to 19 years can occur with hydranencephaly, even without rostral brain regions, with isoelectric electroencephalograms, and with absent-evoked potentials. Finally, the ethical aspects of these findings, as they relate to anencephaly and organ transplantation, are discussed. |
| doi_str_mv | 10.1016/S0887-8994(00)00154-5 |
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Rarely, patients with prolonged survival have been reported, but these infants may have had other neurologic conditions that mimicked hydranencephaly, such as massive hydrocephalus or holoprosencephaly. We report two infants with prenatally acquired hydranencephaly who survived for 66 and 24 months. We reviewed published reports to ascertain the clinical and laboratory features associated with survival of more than 6 months. This review demonstrates that prolonged survival up to 19 years can occur with hydranencephaly, even without rostral brain regions, with isoelectric electroencephalograms, and with absent-evoked potentials. 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Rarely, patients with prolonged survival have been reported, but these infants may have had other neurologic conditions that mimicked hydranencephaly, such as massive hydrocephalus or holoprosencephaly. We report two infants with prenatally acquired hydranencephaly who survived for 66 and 24 months. We reviewed published reports to ascertain the clinical and laboratory features associated with survival of more than 6 months. This review demonstrates that prolonged survival up to 19 years can occur with hydranencephaly, even without rostral brain regions, with isoelectric electroencephalograms, and with absent-evoked potentials. Finally, the ethical aspects of these findings, as they relate to anencephaly and organ transplantation, are discussed.</description><subject>Biological and medical sciences</subject><subject>Brain - abnormalities</subject><subject>Brain - diagnostic imaging</subject><subject>Brain - physiopathology</subject><subject>Brain Death - legislation & jurisprudence</subject><subject>Brain Death - physiopathology</subject><subject>Child, Preschool</subject><subject>Electroencephalography</subject><subject>Ethics, Medical</subject><subject>Humans</subject><subject>Hydranencephaly - diagnostic imaging</subject><subject>Hydranencephaly - mortality</subject><subject>Life Expectancy</subject><subject>Male</subject><subject>Malformations of the nervous system</subject><subject>Medical sciences</subject><subject>Neurology</subject><subject>Prognosis</subject><subject>Tissue and Organ Harvesting - legislation & jurisprudence</subject><subject>Tomography, X-Ray Computed</subject><subject>United States</subject><subject>Ventriculoperitoneal Shunt</subject><issn>0887-8994</issn><issn>1873-5150</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2000</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqF0M9rFDEUwPEgFrtW_wQlBxE9jL5MfkzSi0hRKxQUtOeQSTJuZHYyJpld9r83211sb55y-byXxxehFwTeESDi_Q-QsmukUuwNwFsAwlnDH6EVkR1tOOHwGK3-kXP0NOffAMBVy56gcwJKUNXJFbr9nuIYp1_e4bykbdiaEe9CWeP13iUz-cn6eW3G_SVOfo6p4Djgsot4NiX4qWRsJofHUHwyZUm-qm3wu2fobDBj9s9P7wW6_fzp59V1c_Pty9erjzeNpQpKQxUXihOluBSCycHTXpneA1OEtcQZ0raeO6coEX3HB9eJ3lgujCEKZAsDvUCvj3vnFP8sPhe9Cdn6cayXxyXrrm0JoUJWyI_Qpphz8oOeU9iYtNcE9KGnvuupD7E0gL7rqXmde3n6YOk33j2YOgas4NUJmGzNONRmNuR7xzrGKFT24ch8rVELJZ1tOMR1IXlbtIvhP5f8BRppkks</recordid><startdate>20000701</startdate><enddate>20000701</enddate><creator>McAbee, Gary N</creator><creator>Chan, Allison</creator><creator>Erde, Edmund L</creator><general>Elsevier Inc</general><general>Elsevier</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>20000701</creationdate><title>Prolonged survival with hydranencephaly: report of two patients and literature review</title><author>McAbee, Gary N ; Chan, Allison ; Erde, Edmund L</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c390t-395695199586648fe3b9abe0491421da122e5dd9316b75fd76bac56aa190820f3</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2000</creationdate><topic>Biological and medical sciences</topic><topic>Brain - abnormalities</topic><topic>Brain - diagnostic imaging</topic><topic>Brain - physiopathology</topic><topic>Brain Death - legislation & jurisprudence</topic><topic>Brain Death - physiopathology</topic><topic>Child, Preschool</topic><topic>Electroencephalography</topic><topic>Ethics, Medical</topic><topic>Humans</topic><topic>Hydranencephaly - diagnostic imaging</topic><topic>Hydranencephaly - mortality</topic><topic>Life Expectancy</topic><topic>Male</topic><topic>Malformations of the nervous system</topic><topic>Medical sciences</topic><topic>Neurology</topic><topic>Prognosis</topic><topic>Tissue and Organ Harvesting - legislation & jurisprudence</topic><topic>Tomography, X-Ray Computed</topic><topic>United States</topic><topic>Ventriculoperitoneal Shunt</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>McAbee, Gary N</creatorcontrib><creatorcontrib>Chan, Allison</creatorcontrib><creatorcontrib>Erde, Edmund L</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Pediatric neurology</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>McAbee, Gary N</au><au>Chan, Allison</au><au>Erde, Edmund L</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Prolonged survival with hydranencephaly: report of two patients and literature review</atitle><jtitle>Pediatric neurology</jtitle><addtitle>Pediatr Neurol</addtitle><date>2000-07-01</date><risdate>2000</risdate><volume>23</volume><issue>1</issue><spage>80</spage><epage>84</epage><pages>80-84</pages><issn>0887-8994</issn><eissn>1873-5150</eissn><abstract>Infants with hydranencephaly are presumed to have a reduced life expectancy, with a survival of several weeks to months. 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| ispartof | Pediatric neurology, 2000-07, Vol.23 (1), p.80-84 |
| issn | 0887-8994 1873-5150 |
| language | eng |
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| source | MEDLINE; Elsevier ScienceDirect Journals Complete |
| subjects | Biological and medical sciences Brain - abnormalities Brain - diagnostic imaging Brain - physiopathology Brain Death - legislation & jurisprudence Brain Death - physiopathology Child, Preschool Electroencephalography Ethics, Medical Humans Hydranencephaly - diagnostic imaging Hydranencephaly - mortality Life Expectancy Male Malformations of the nervous system Medical sciences Neurology Prognosis Tissue and Organ Harvesting - legislation & jurisprudence Tomography, X-Ray Computed United States Ventriculoperitoneal Shunt |
| title | Prolonged survival with hydranencephaly: report of two patients and literature review |
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