The Outcome of Children Born with Pulmonary Atresia and Intact Ventricular Septum in Sweden from 1980 to 1999
Objective - To study the outcome of all children born with pulmonary atresia and intact ventricular septum in Sweden between 1980 and 1999. Design - Retrospective study of medical records with review of the initial, preoperative angiocardiographic and echocardiographic examinations. Results - A tota...
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| Veröffentlicht in: | Scandinavian cardiovascular journal : SCJ 2001, Vol.35 (3), p.192-198 |
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| creator | JOELSSON, B.-M. Ekman SUNNEGARDH, J HANSEUS, K BERGGREN, H JONZON, A JÖGI, P LUNDELL, B |
| description | Objective - To study the outcome of all children born with pulmonary atresia and intact ventricular septum in Sweden between 1980 and 1999. Design - Retrospective study of medical records with review of the initial, preoperative angiocardiographic and echocardiographic examinations. Results - A total of 84 children were born with pulmonary atresia and intact ventricular septum, giving an incidence of 4.2 per 100 000 live births. In all, 77 were operated on with a 1-year survival rate of 75%. Thirty-six children had ventriculocoronary communications, with a 1-year survival rate of 50%. At the end of the study period, 52 children were alive, 32 with biventricular repair, and 19 with univentricular repair. Follow-up time was 14 days-20 years (median, 6 years). Statistical analysis of incremental risk factors for death showed statistical significance for low birth weight, male sex, muscular pulmonary atresia, and having a systemic-to-pulmonary shunt as the sole initial intervention. Conclusion - Complete national data of all patients born with pulmonary atresia and intact ventricular septum during 1980-1999 in Sweden revealed a total mortality in accordance with previous reports for results for surgery. Further improvements demand a thorough preoperative investigation of the cardiac anatomy, particularly of the ventriculocoronary communications, to enable right ventricular decompression whenever possible. |
| doi_str_mv | 10.1080/140174301750305072 |
| format | Article |
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Ekman ; SUNNEGARDH, J ; HANSEUS, K ; BERGGREN, H ; JONZON, A ; JÖGI, P ; LUNDELL, B</creator><creatorcontrib>JOELSSON, B.-M. Ekman ; SUNNEGARDH, J ; HANSEUS, K ; BERGGREN, H ; JONZON, A ; JÖGI, P ; LUNDELL, B</creatorcontrib><description>Objective - To study the outcome of all children born with pulmonary atresia and intact ventricular septum in Sweden between 1980 and 1999. Design - Retrospective study of medical records with review of the initial, preoperative angiocardiographic and echocardiographic examinations. Results - A total of 84 children were born with pulmonary atresia and intact ventricular septum, giving an incidence of 4.2 per 100 000 live births. In all, 77 were operated on with a 1-year survival rate of 75%. Thirty-six children had ventriculocoronary communications, with a 1-year survival rate of 50%. At the end of the study period, 52 children were alive, 32 with biventricular repair, and 19 with univentricular repair. Follow-up time was 14 days-20 years (median, 6 years). Statistical analysis of incremental risk factors for death showed statistical significance for low birth weight, male sex, muscular pulmonary atresia, and having a systemic-to-pulmonary shunt as the sole initial intervention. Conclusion - Complete national data of all patients born with pulmonary atresia and intact ventricular septum during 1980-1999 in Sweden revealed a total mortality in accordance with previous reports for results for surgery. Further improvements demand a thorough preoperative investigation of the cardiac anatomy, particularly of the ventriculocoronary communications, to enable right ventricular decompression whenever possible.</description><identifier>ISSN: 1401-7431</identifier><identifier>EISSN: 1651-2006</identifier><identifier>DOI: 10.1080/140174301750305072</identifier><identifier>PMID: 11515692</identifier><language>eng</language><publisher>Copenhagen: Informa UK Ltd</publisher><subject>Biological and medical sciences ; Cardiology and Cardiovascular Disease ; Cardiology. Vascular system ; Child ; Child, Preschool ; Children Long-TERM Follow-UP Pulmonary Atresia And Intact Ventricular Septum Surgery ; Electrocardiography ; Female ; Heart ; Heart Septal Defects ; Heart Septal Defects - physiopathology ; Heart Septal Defects - surgery ; Heart Septum ; Heart Septum - physiopathology ; Heart Septum - surgery ; Humans ; Infant ; Infant, Newborn ; Kardiologi och kardiovaskulära sjukdomar ; Male ; Medical sciences ; Newborn ; physiopathology ; Preschool ; Pulmonary Atresia ; Pulmonary Atresia - physiopathology ; Pulmonary Atresia - surgery ; surgery ; Sweden ; Treatment Outcome ; Tumors of the heart</subject><ispartof>Scandinavian cardiovascular journal : SCJ, 2001, Vol.35 (3), p.192-198</ispartof><rights>2001 Informa UK Ltd All rights reserved: reproduction in whole or part not permitted 2001</rights><rights>2002 INIST-CNRS</rights><lds50>peer_reviewed</lds50><oa>free_for_read</oa><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c556t-ee673695c6e10ed9423c80a990d05c55d228ad47c9dda85773b6daa9f78f81d63</citedby><cites>FETCH-LOGICAL-c556t-ee673695c6e10ed9423c80a990d05c55d228ad47c9dda85773b6daa9f78f81d63</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktopdf>$$Uhttps://www.tandfonline.com/doi/pdf/10.1080/140174301750305072$$EPDF$$P50$$Ginformahealthcare$$H</linktopdf><linktohtml>$$Uhttps://www.tandfonline.com/doi/full/10.1080/140174301750305072$$EHTML$$P50$$Ginformahealthcare$$H</linktohtml><link.rule.ids>230,314,776,780,881,4010,27900,27901,27902,59620,60409,61194,61375</link.rule.ids><backlink>$$Uhttp://pascal-francis.inist.fr/vibad/index.php?action=getRecordDetail&idt=14100562$$DView record in Pascal Francis$$Hfree_for_read</backlink><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/11515692$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink><backlink>$$Uhttps://gup.ub.gu.se/publication/123606$$DView record from Swedish Publication Index$$Hfree_for_read</backlink><backlink>$$Uhttp://kipublications.ki.se/Default.aspx?queryparsed=id:1939590$$DView record from Swedish Publication Index$$Hfree_for_read</backlink></links><search><creatorcontrib>JOELSSON, B.-M. Ekman</creatorcontrib><creatorcontrib>SUNNEGARDH, J</creatorcontrib><creatorcontrib>HANSEUS, K</creatorcontrib><creatorcontrib>BERGGREN, H</creatorcontrib><creatorcontrib>JONZON, A</creatorcontrib><creatorcontrib>JÖGI, P</creatorcontrib><creatorcontrib>LUNDELL, B</creatorcontrib><title>The Outcome of Children Born with Pulmonary Atresia and Intact Ventricular Septum in Sweden from 1980 to 1999</title><title>Scandinavian cardiovascular journal : SCJ</title><addtitle>Scand Cardiovasc J</addtitle><description>Objective - To study the outcome of all children born with pulmonary atresia and intact ventricular septum in Sweden between 1980 and 1999. Design - Retrospective study of medical records with review of the initial, preoperative angiocardiographic and echocardiographic examinations. Results - A total of 84 children were born with pulmonary atresia and intact ventricular septum, giving an incidence of 4.2 per 100 000 live births. In all, 77 were operated on with a 1-year survival rate of 75%. Thirty-six children had ventriculocoronary communications, with a 1-year survival rate of 50%. At the end of the study period, 52 children were alive, 32 with biventricular repair, and 19 with univentricular repair. Follow-up time was 14 days-20 years (median, 6 years). Statistical analysis of incremental risk factors for death showed statistical significance for low birth weight, male sex, muscular pulmonary atresia, and having a systemic-to-pulmonary shunt as the sole initial intervention. Conclusion - Complete national data of all patients born with pulmonary atresia and intact ventricular septum during 1980-1999 in Sweden revealed a total mortality in accordance with previous reports for results for surgery. Further improvements demand a thorough preoperative investigation of the cardiac anatomy, particularly of the ventriculocoronary communications, to enable right ventricular decompression whenever possible.</description><subject>Biological and medical sciences</subject><subject>Cardiology and Cardiovascular Disease</subject><subject>Cardiology. Vascular system</subject><subject>Child</subject><subject>Child, Preschool</subject><subject>Children Long-TERM Follow-UP Pulmonary Atresia And Intact Ventricular Septum Surgery</subject><subject>Electrocardiography</subject><subject>Female</subject><subject>Heart</subject><subject>Heart Septal Defects</subject><subject>Heart Septal Defects - physiopathology</subject><subject>Heart Septal Defects - surgery</subject><subject>Heart Septum</subject><subject>Heart Septum - physiopathology</subject><subject>Heart Septum - surgery</subject><subject>Humans</subject><subject>Infant</subject><subject>Infant, Newborn</subject><subject>Kardiologi och kardiovaskulära sjukdomar</subject><subject>Male</subject><subject>Medical sciences</subject><subject>Newborn</subject><subject>physiopathology</subject><subject>Preschool</subject><subject>Pulmonary Atresia</subject><subject>Pulmonary Atresia - physiopathology</subject><subject>Pulmonary Atresia - surgery</subject><subject>surgery</subject><subject>Sweden</subject><subject>Treatment Outcome</subject><subject>Tumors of the heart</subject><issn>1401-7431</issn><issn>1651-2006</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2001</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNp9kU1rFEEQhgdRTIz-AQ_SF72NVs1s90yDHuLiRyAQIdFr09tdk5040732B0v-vb3sahBhL1VF8bwvVbxV9RLhLUIP73AB2C3aUji0wKFrHlWnKDjWDYB4XOYC1IXAk-pZjHcAyHuOT6sTRI5cyOa0mm_WxK5yMn4m5ge2XI-TDeTYRx8c245pzb7lafZOh3t2ngLFUTPtLLtwSZvEfpBLYTR50oFd0yblmY2OXW_JFo8h-Jmh7IElX7qUz6sng54ivTj0s-r75083y6_15dWXi-X5ZW04F6kmEl0rJDeCEMjKRdOaHrSUYIEXxDZNr-2iM9Ja3fOua1fCai2Hrh96tKI9q-q9b9zSJq_UJoxzeUB5ParD6meZSHEpJDRH-du8UWV1m3c8Nq2Anf-bPb8J_lemmNQ8RkPTpB35HFWHiI1ouwI2e9AEH2Og4a81gtqFqP4PsYheHdzzaib7IDmkVoDXB0BHo6chaGfG-MAtEICLHfdhz41u8GHWWx8mq5K-n3z4I2qPHvL-H_2a9JTWRgdSdz4HVyI89sdvKXrI5Q</recordid><startdate>2001</startdate><enddate>2001</enddate><creator>JOELSSON, B.-M. Ekman</creator><creator>SUNNEGARDH, J</creator><creator>HANSEUS, K</creator><creator>BERGGREN, H</creator><creator>JONZON, A</creator><creator>JÖGI, P</creator><creator>LUNDELL, B</creator><general>Informa UK Ltd</general><general>Taylor & Francis</general><general>Scandinavian University Press</general><scope>IQODW</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope><scope>ADTPV</scope><scope>AOWAS</scope><scope>F1U</scope></search><sort><creationdate>2001</creationdate><title>The Outcome of Children Born with Pulmonary Atresia and Intact Ventricular Septum in Sweden from 1980 to 1999</title><author>JOELSSON, B.-M. Ekman ; SUNNEGARDH, J ; HANSEUS, K ; BERGGREN, H ; JONZON, A ; JÖGI, P ; LUNDELL, B</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c556t-ee673695c6e10ed9423c80a990d05c55d228ad47c9dda85773b6daa9f78f81d63</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2001</creationdate><topic>Biological and medical sciences</topic><topic>Cardiology and Cardiovascular Disease</topic><topic>Cardiology. Vascular system</topic><topic>Child</topic><topic>Child, Preschool</topic><topic>Children Long-TERM Follow-UP Pulmonary Atresia And Intact Ventricular Septum Surgery</topic><topic>Electrocardiography</topic><topic>Female</topic><topic>Heart</topic><topic>Heart Septal Defects</topic><topic>Heart Septal Defects - physiopathology</topic><topic>Heart Septal Defects - surgery</topic><topic>Heart Septum</topic><topic>Heart Septum - physiopathology</topic><topic>Heart Septum - surgery</topic><topic>Humans</topic><topic>Infant</topic><topic>Infant, Newborn</topic><topic>Kardiologi och kardiovaskulära sjukdomar</topic><topic>Male</topic><topic>Medical sciences</topic><topic>Newborn</topic><topic>physiopathology</topic><topic>Preschool</topic><topic>Pulmonary Atresia</topic><topic>Pulmonary Atresia - physiopathology</topic><topic>Pulmonary Atresia - surgery</topic><topic>surgery</topic><topic>Sweden</topic><topic>Treatment Outcome</topic><topic>Tumors of the heart</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>JOELSSON, B.-M. Ekman</creatorcontrib><creatorcontrib>SUNNEGARDH, J</creatorcontrib><creatorcontrib>HANSEUS, K</creatorcontrib><creatorcontrib>BERGGREN, H</creatorcontrib><creatorcontrib>JONZON, A</creatorcontrib><creatorcontrib>JÖGI, P</creatorcontrib><creatorcontrib>LUNDELL, B</creatorcontrib><collection>Pascal-Francis</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><collection>SwePub</collection><collection>SwePub Articles</collection><collection>SWEPUB Göteborgs universitet</collection><jtitle>Scandinavian cardiovascular journal : SCJ</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>JOELSSON, B.-M. Ekman</au><au>SUNNEGARDH, J</au><au>HANSEUS, K</au><au>BERGGREN, H</au><au>JONZON, A</au><au>JÖGI, P</au><au>LUNDELL, B</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>The Outcome of Children Born with Pulmonary Atresia and Intact Ventricular Septum in Sweden from 1980 to 1999</atitle><jtitle>Scandinavian cardiovascular journal : SCJ</jtitle><addtitle>Scand Cardiovasc J</addtitle><date>2001</date><risdate>2001</risdate><volume>35</volume><issue>3</issue><spage>192</spage><epage>198</epage><pages>192-198</pages><issn>1401-7431</issn><eissn>1651-2006</eissn><abstract>Objective - To study the outcome of all children born with pulmonary atresia and intact ventricular septum in Sweden between 1980 and 1999. Design - Retrospective study of medical records with review of the initial, preoperative angiocardiographic and echocardiographic examinations. Results - A total of 84 children were born with pulmonary atresia and intact ventricular septum, giving an incidence of 4.2 per 100 000 live births. In all, 77 were operated on with a 1-year survival rate of 75%. Thirty-six children had ventriculocoronary communications, with a 1-year survival rate of 50%. At the end of the study period, 52 children were alive, 32 with biventricular repair, and 19 with univentricular repair. Follow-up time was 14 days-20 years (median, 6 years). Statistical analysis of incremental risk factors for death showed statistical significance for low birth weight, male sex, muscular pulmonary atresia, and having a systemic-to-pulmonary shunt as the sole initial intervention. Conclusion - Complete national data of all patients born with pulmonary atresia and intact ventricular septum during 1980-1999 in Sweden revealed a total mortality in accordance with previous reports for results for surgery. Further improvements demand a thorough preoperative investigation of the cardiac anatomy, particularly of the ventriculocoronary communications, to enable right ventricular decompression whenever possible.</abstract><cop>Copenhagen</cop><cop>Oslo</cop><cop>Stockholm</cop><pub>Informa UK Ltd</pub><pmid>11515692</pmid><doi>10.1080/140174301750305072</doi><tpages>7</tpages><oa>free_for_read</oa></addata></record> |
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| subjects | Biological and medical sciences Cardiology and Cardiovascular Disease Cardiology. Vascular system Child Child, Preschool Children Long-TERM Follow-UP Pulmonary Atresia And Intact Ventricular Septum Surgery Electrocardiography Female Heart Heart Septal Defects Heart Septal Defects - physiopathology Heart Septal Defects - surgery Heart Septum Heart Septum - physiopathology Heart Septum - surgery Humans Infant Infant, Newborn Kardiologi och kardiovaskulära sjukdomar Male Medical sciences Newborn physiopathology Preschool Pulmonary Atresia Pulmonary Atresia - physiopathology Pulmonary Atresia - surgery surgery Sweden Treatment Outcome Tumors of the heart |
| title | The Outcome of Children Born with Pulmonary Atresia and Intact Ventricular Septum in Sweden from 1980 to 1999 |
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