Lymphangioleiomyomatosis: a case report
Lymphangioleiomyomatosis (LAM) is a rare disease of unknown etiology affecting woman, primarily in their reproductive years. It is characterized by non-neoplasic proliferation of atypical smooth muscle cells that may lead to airway, lymphatic and blood vessel obstruction over time.A nine-year follow...
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| Veröffentlicht in: | Revista portuguesa de pneumologia 2005-11, Vol.11 (6), p.573-586 |
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| container_title | Revista portuguesa de pneumologia |
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| creator | Costa, Antonio Santos Noya, Rafael Calvo, Teresa Campos Severo, R Afonso, Abel |
| description | Lymphangioleiomyomatosis (LAM) is a rare disease of unknown etiology affecting woman, primarily in their reproductive years. It is characterized by non-neoplasic proliferation of atypical smooth muscle cells that may lead to airway, lymphatic and blood vessel obstruction over time.A nine-year followed-up case of LAM is described,which presents with some unusual details as worsening haemoptysis in the setting of pregnancy and absence of cough or pneumothorax along the course of the disease. Neither haemoptysis nor gradual pulmonary function deterioration seemed to be influenced by hormone therapy. A brief re-view of the disease is then presented. |
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It is characterized by non-neoplasic proliferation of atypical smooth muscle cells that may lead to airway, lymphatic and blood vessel obstruction over time.A nine-year followed-up case of LAM is described,which presents with some unusual details as worsening haemoptysis in the setting of pregnancy and absence of cough or pneumothorax along the course of the disease. Neither haemoptysis nor gradual pulmonary function deterioration seemed to be influenced by hormone therapy. 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| source | MEDLINE; Elsevier ScienceDirect Journals Complete; DOAJ Directory of Open Access Journals; Elektronische Zeitschriftenbibliothek - Frei zugängliche E-Journals; Alma/SFX Local Collection |
| subjects | Adult Female Humans Lung Neoplasms - diagnosis Lymphangioleiomyomatosis - diagnosis Pregnancy Pregnancy Complications, Neoplastic - diagnosis |
| title | Lymphangioleiomyomatosis: a case report |
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