Cardiac and Great Vessel Involvement in "Behcet's Disease"
Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracav...
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Veröffentlicht in: | Journal of cardiac surgery 2008-11, Vol.23 (6), p.765-768 |
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container_title | Journal of cardiac surgery |
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creator | Marzban, Mehrab Mandegar, Mohammad Hossein Karimi, Abbasali Abbasi, Kyomars Movahedi, Namvar Navabi, Mohammad Ali Abbasi, Seyed Hesameddin Moshtaghi, Naghmeh |
description | Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch. |
doi_str_mv | 10.1111/j.1540-8191.2008.00607.x |
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Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.</description><identifier>ISSN: 0886-0440</identifier><identifier>EISSN: 1540-8191</identifier><identifier>DOI: 10.1111/j.1540-8191.2008.00607.x</identifier><identifier>PMID: 19017008</identifier><language>eng</language><publisher>Malden, USA: Blackwell Publishing Inc</publisher><subject>Adult ; Aneurysm - etiology ; Aneurysm - surgery ; Aneurysm, False - pathology ; Aneurysm, False - surgery ; Aortic Aneurysm - etiology ; Aortic Aneurysm, Abdominal - etiology ; Aortic Aneurysm, Thoracic - etiology ; Behcet Syndrome - complications ; Behcet Syndrome - diagnosis ; Behcet Syndrome - physiopathology ; Behcet Syndrome - surgery ; Cardiac Surgical Procedures ; Cardiovascular Diseases - etiology ; Cardiovascular Diseases - mortality ; Cardiovascular Diseases - surgery ; Fatal Outcome ; Female ; Humans ; Male ; Middle Aged ; Pulmonary Artery - pathology</subject><ispartof>Journal of cardiac surgery, 2008-11, Vol.23 (6), p.765-768</ispartof><rights>2008 Wiley Periodicals, Inc.</rights><lds50>peer_reviewed</lds50><oa>free_for_read</oa><woscitedreferencessubscribed>false</woscitedreferencessubscribed><citedby>FETCH-LOGICAL-c4557-c46a5dcea8f43102d4a3754f3782db0ad9d06dac1a30b42b91905e9fbfbde9c33</citedby><cites>FETCH-LOGICAL-c4557-c46a5dcea8f43102d4a3754f3782db0ad9d06dac1a30b42b91905e9fbfbde9c33</cites></display><links><openurl>$$Topenurl_article</openurl><openurlfulltext>$$Topenurlfull_article</openurlfulltext><thumbnail>$$Tsyndetics_thumb_exl</thumbnail><linktopdf>$$Uhttps://onlinelibrary.wiley.com/doi/pdf/10.1111%2Fj.1540-8191.2008.00607.x$$EPDF$$P50$$Gwiley$$H</linktopdf><linktohtml>$$Uhttps://onlinelibrary.wiley.com/doi/full/10.1111%2Fj.1540-8191.2008.00607.x$$EHTML$$P50$$Gwiley$$H</linktohtml><link.rule.ids>314,776,780,1411,27901,27902,45550,45551</link.rule.ids><backlink>$$Uhttps://www.ncbi.nlm.nih.gov/pubmed/19017008$$D View this record in MEDLINE/PubMed$$Hfree_for_read</backlink></links><search><creatorcontrib>Marzban, Mehrab</creatorcontrib><creatorcontrib>Mandegar, Mohammad Hossein</creatorcontrib><creatorcontrib>Karimi, Abbasali</creatorcontrib><creatorcontrib>Abbasi, Kyomars</creatorcontrib><creatorcontrib>Movahedi, Namvar</creatorcontrib><creatorcontrib>Navabi, Mohammad Ali</creatorcontrib><creatorcontrib>Abbasi, Seyed Hesameddin</creatorcontrib><creatorcontrib>Moshtaghi, Naghmeh</creatorcontrib><title>Cardiac and Great Vessel Involvement in "Behcet's Disease"</title><title>Journal of cardiac surgery</title><addtitle>J Card Surg</addtitle><description>Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.</description><subject>Adult</subject><subject>Aneurysm - etiology</subject><subject>Aneurysm - surgery</subject><subject>Aneurysm, False - pathology</subject><subject>Aneurysm, False - surgery</subject><subject>Aortic Aneurysm - etiology</subject><subject>Aortic Aneurysm, Abdominal - etiology</subject><subject>Aortic Aneurysm, Thoracic - etiology</subject><subject>Behcet Syndrome - complications</subject><subject>Behcet Syndrome - diagnosis</subject><subject>Behcet Syndrome - physiopathology</subject><subject>Behcet Syndrome - surgery</subject><subject>Cardiac Surgical Procedures</subject><subject>Cardiovascular Diseases - etiology</subject><subject>Cardiovascular Diseases - mortality</subject><subject>Cardiovascular Diseases - surgery</subject><subject>Fatal Outcome</subject><subject>Female</subject><subject>Humans</subject><subject>Male</subject><subject>Middle Aged</subject><subject>Pulmonary Artery - pathology</subject><issn>0886-0440</issn><issn>1540-8191</issn><fulltext>true</fulltext><rsrctype>article</rsrctype><creationdate>2008</creationdate><recordtype>article</recordtype><sourceid>EIF</sourceid><recordid>eNqNkF1PwjAUhhujEUT_glm40KvN07XbOhMvFBUxRgzix13TrWdxOAauA-HfW4Tgrb1oT9L3OefkIcSh4FF7zkYeDTi4gsbU8wGEBxBC5C12SHP7sUuaIEToAufQIAfGjAB8nzPYJw0aA40s1yTnHVXpXKWOKrXTrVDVzisag4XTK-eTYo5jLGsnL532FX6kWJ8a5zo3qAy2D8lepgqDR5u3RV5ub4adO_eh3-11Lh_clAdBZO9QBTpFJTLOKPiaKxYFPGOR8HUCSscaQq1Sqhgk3E9iu1yAcZZkicY4ZaxFTtZ9p9Xka4amluPcpFgUqsTJzMgwFhAFIrRBsQ6m1cSYCjM5rfKxqpaSglx5kyO50iNXeuTKm_z1JhcWPd7MmCVj1H_gRpQNXKwD33mBy383lvf9zrOtLO-u-dzUuNjyqvqUYWR9yLfHrnwa0CFlg0i-sx90aYmM</recordid><startdate>200811</startdate><enddate>200811</enddate><creator>Marzban, Mehrab</creator><creator>Mandegar, Mohammad Hossein</creator><creator>Karimi, Abbasali</creator><creator>Abbasi, Kyomars</creator><creator>Movahedi, Namvar</creator><creator>Navabi, Mohammad Ali</creator><creator>Abbasi, Seyed Hesameddin</creator><creator>Moshtaghi, Naghmeh</creator><general>Blackwell Publishing Inc</general><scope>BSCLL</scope><scope>CGR</scope><scope>CUY</scope><scope>CVF</scope><scope>ECM</scope><scope>EIF</scope><scope>NPM</scope><scope>AAYXX</scope><scope>CITATION</scope><scope>7X8</scope></search><sort><creationdate>200811</creationdate><title>Cardiac and Great Vessel Involvement in "Behcet's Disease"</title><author>Marzban, Mehrab ; Mandegar, Mohammad Hossein ; Karimi, Abbasali ; Abbasi, Kyomars ; Movahedi, Namvar ; Navabi, Mohammad Ali ; Abbasi, Seyed Hesameddin ; Moshtaghi, Naghmeh</author></sort><facets><frbrtype>5</frbrtype><frbrgroupid>cdi_FETCH-LOGICAL-c4557-c46a5dcea8f43102d4a3754f3782db0ad9d06dac1a30b42b91905e9fbfbde9c33</frbrgroupid><rsrctype>articles</rsrctype><prefilter>articles</prefilter><language>eng</language><creationdate>2008</creationdate><topic>Adult</topic><topic>Aneurysm - etiology</topic><topic>Aneurysm - surgery</topic><topic>Aneurysm, False - pathology</topic><topic>Aneurysm, False - surgery</topic><topic>Aortic Aneurysm - etiology</topic><topic>Aortic Aneurysm, Abdominal - etiology</topic><topic>Aortic Aneurysm, Thoracic - etiology</topic><topic>Behcet Syndrome - complications</topic><topic>Behcet Syndrome - diagnosis</topic><topic>Behcet Syndrome - physiopathology</topic><topic>Behcet Syndrome - surgery</topic><topic>Cardiac Surgical Procedures</topic><topic>Cardiovascular Diseases - etiology</topic><topic>Cardiovascular Diseases - mortality</topic><topic>Cardiovascular Diseases - surgery</topic><topic>Fatal Outcome</topic><topic>Female</topic><topic>Humans</topic><topic>Male</topic><topic>Middle Aged</topic><topic>Pulmonary Artery - pathology</topic><toplevel>peer_reviewed</toplevel><toplevel>online_resources</toplevel><creatorcontrib>Marzban, Mehrab</creatorcontrib><creatorcontrib>Mandegar, Mohammad Hossein</creatorcontrib><creatorcontrib>Karimi, Abbasali</creatorcontrib><creatorcontrib>Abbasi, Kyomars</creatorcontrib><creatorcontrib>Movahedi, Namvar</creatorcontrib><creatorcontrib>Navabi, Mohammad Ali</creatorcontrib><creatorcontrib>Abbasi, Seyed Hesameddin</creatorcontrib><creatorcontrib>Moshtaghi, Naghmeh</creatorcontrib><collection>Istex</collection><collection>Medline</collection><collection>MEDLINE</collection><collection>MEDLINE (Ovid)</collection><collection>MEDLINE</collection><collection>MEDLINE</collection><collection>PubMed</collection><collection>CrossRef</collection><collection>MEDLINE - Academic</collection><jtitle>Journal of cardiac surgery</jtitle></facets><delivery><delcategory>Remote Search Resource</delcategory><fulltext>fulltext</fulltext></delivery><addata><au>Marzban, Mehrab</au><au>Mandegar, Mohammad Hossein</au><au>Karimi, Abbasali</au><au>Abbasi, Kyomars</au><au>Movahedi, Namvar</au><au>Navabi, Mohammad Ali</au><au>Abbasi, Seyed Hesameddin</au><au>Moshtaghi, Naghmeh</au><format>journal</format><genre>article</genre><ristype>JOUR</ristype><atitle>Cardiac and Great Vessel Involvement in "Behcet's Disease"</atitle><jtitle>Journal of cardiac surgery</jtitle><addtitle>J Card Surg</addtitle><date>2008-11</date><risdate>2008</risdate><volume>23</volume><issue>6</issue><spage>765</spage><epage>768</epage><pages>765-768</pages><issn>0886-0440</issn><eissn>1540-8191</eissn><abstract>Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.</abstract><cop>Malden, USA</cop><pub>Blackwell Publishing Inc</pub><pmid>19017008</pmid><doi>10.1111/j.1540-8191.2008.00607.x</doi><tpages>4</tpages><oa>free_for_read</oa></addata></record> |
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subjects | Adult Aneurysm - etiology Aneurysm - surgery Aneurysm, False - pathology Aneurysm, False - surgery Aortic Aneurysm - etiology Aortic Aneurysm, Abdominal - etiology Aortic Aneurysm, Thoracic - etiology Behcet Syndrome - complications Behcet Syndrome - diagnosis Behcet Syndrome - physiopathology Behcet Syndrome - surgery Cardiac Surgical Procedures Cardiovascular Diseases - etiology Cardiovascular Diseases - mortality Cardiovascular Diseases - surgery Fatal Outcome Female Humans Male Middle Aged Pulmonary Artery - pathology |
title | Cardiac and Great Vessel Involvement in "Behcet's Disease" |
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