Cardiac and Great Vessel Involvement in "Behcet's Disease"

Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracav...

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Veröffentlicht in:Journal of cardiac surgery 2008-11, Vol.23 (6), p.765-768
Hauptverfasser: Marzban, Mehrab, Mandegar, Mohammad Hossein, Karimi, Abbasali, Abbasi, Kyomars, Movahedi, Namvar, Navabi, Mohammad Ali, Abbasi, Seyed Hesameddin, Moshtaghi, Naghmeh
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container_end_page 768
container_issue 6
container_start_page 765
container_title Journal of cardiac surgery
container_volume 23
creator Marzban, Mehrab
Mandegar, Mohammad Hossein
Karimi, Abbasali
Abbasi, Kyomars
Movahedi, Namvar
Navabi, Mohammad Ali
Abbasi, Seyed Hesameddin
Moshtaghi, Naghmeh
description Behcet's disease is a multisystem disorder and classified as “vasculitic syndrome with a wide variety of clinical manifestations.” Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.
doi_str_mv 10.1111/j.1540-8191.2008.00607.x
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Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. 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subjects Adult
Aneurysm - etiology
Aneurysm - surgery
Aneurysm, False - pathology
Aneurysm, False - surgery
Aortic Aneurysm - etiology
Aortic Aneurysm, Abdominal - etiology
Aortic Aneurysm, Thoracic - etiology
Behcet Syndrome - complications
Behcet Syndrome - diagnosis
Behcet Syndrome - physiopathology
Behcet Syndrome - surgery
Cardiac Surgical Procedures
Cardiovascular Diseases - etiology
Cardiovascular Diseases - mortality
Cardiovascular Diseases - surgery
Fatal Outcome
Female
Humans
Male
Middle Aged
Pulmonary Artery - pathology
title Cardiac and Great Vessel Involvement in "Behcet's Disease"
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